• 제목/요약/키워드: Congenital cystic adenoid malformation

검색결과 4건 처리시간 0.024초

성인에서 발견된 선천성 낭성 선종양기형 1예 (A Case of Congenital Cystic Adenomatoid Malformation(CCAM) of the Lung in Adult)

  • 조용선;이양덕;한민수;강동욱
    • Tuberculosis and Respiratory Diseases
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    • 제55권1호
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    • pp.107-112
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    • 2003
  • A congenital cystic adenoid malformation of the lung(CCAM) is characterized by an anomalous fetal development of the terminal respiratory structures, resulting in the adenomatoid proliferation of the bronchiolar elements and cystic formation. CCAM has been detected on the fetus, premature babies and stillborn as well as infants and children. An adult presentation of CCAM is extremely rare. When cystic lesions occur with a repeated infection, an evaluation of the cystic lesions requires a differential diagnosis of CCAM, sequestration, a lung abscess, a pneumatocele and a bronchogenic cyst. The definite treatment of CCAM is the surgical removal of the involved lobe. We report a case of a CCAM in a 24-year-old female with a brief review of the relevant literature.

Life-Threatening Congenital Cystic Adenomatoid Malformation in the Premature Neonate

  • Chong, Yooyoung;Rhee, Youn Ju;Han, Sung Joon;Cho, Hyun Jin;Kang, Shin Kwang;Kang, Min-Woong
    • Journal of Chest Surgery
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    • 제49권3호
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    • pp.210-213
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    • 2016
  • Congenital cystic adenomatoid malformation is a rare, but well-known disease. It can be managed conservatively in patients without symptoms or require surgical removal when symptomatic. The surgical option of choice is en bloc resection of the affected lesion. We report an experience of life-threatening congenital cystic adenoid malformation in a low-birth-weight (1,590 g) premature neonate who was successfully treated with a lobectomy of the lung.

선천성 낭종성 선종양 기형 2례 보 (Congenital cystic adenoid malformation: report of 2 cases)

  • 진성훈;김주현
    • Journal of Chest Surgery
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    • 제17권2호
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    • pp.326-330
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    • 1984
  • Congenital Cystic Adenomatoid Malformation [C.C.A.M], one of lung bud anomalies, is an unusual lesion, only about 200 cases baring been reported by 1980, and characterized by marked proliferation of terminal respiratory structures. Recently we experienced two infants with C.C.A,M., whose clinical courses were quite different. On case 1, the patient was 25-day-old female, and suffered from progressive respiratory distress for 10 days duration. A right middle lobectomy was performed, with a satisfactory postoperative course. On case II, the patient was 7omonth-old male, and admitted for evaluation of known pulmonary anomaly, which was detected for the first time during hospitalization for treatment of pneumonia at 1 month of his age. He underwent a lingular segmentectomy, but died of respiratory insufficiency on postop 10th day. We believe that awareness of the presence of C.C.A.M. is important in making the differential diagnosis of progressive respiratory disease or of recurrent pulmonary infection in infants.

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영양동맥을 동반한 단순 선천성 낭종성 선종양 기형 (Simple Congenital Cystic Adenomatoid Malformation with a Feeding Artery)

  • 김재준;왕영필;박재길
    • Journal of Chest Surgery
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    • 제43권4호
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    • pp.450-453
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    • 2010
  • 선천성 낭종성 선종양 기형은 폐격리증과 같은 다른 동반된 기형 없이는 혈액공급을 폐동맥에서 받는 것으로 알고 있었으나, 저자들의 증례에서는 다른 기형이 동반되지 않은 단순 선천성 낭종성 선종양 기형이 영양동맥을 가지고 있었다. 술 전 영양동맥이 발견되지 않았어도 선천성 낭성 폐질환에서 영양혈관의 가능성에 유의하여야 할 것이다.