• 제목/요약/키워드: Congenital arteriovenous malformation

검색결과 22건 처리시간 0.036초

Congenital Intracranial Vascular Malformations in Children : Radiological Overview

  • Jung-Eun Cheon;Ji Hye Kim
    • Journal of Korean Neurosurgical Society
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    • 제67권3호
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    • pp.270-279
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    • 2024
  • Prompt medical attention is crucial for congenital intracranial vascular malformations in children and newborns due to potential severe outcomes. Imaging is pivotal for accurate identification, given the diverse risks and treatment strategies. This article aims to enhance the identification and understanding of congenital intracranial vascular abnormalities including arteriovenous malformation, arteriovenous fistula, cavernous malformation, capillary telangiectasia, developmental venous anomaly, and sinus pericranii in pediatric patients.

코일 색전술로 치료된 다발성 폐동정맥기형 1 예 (A Case of Multiple Pulmonary Arteriovenous Malformation Treated with Coil Embolization)

  • 안혁수;이흥범;이용철;이양근
    • Tuberculosis and Respiratory Diseases
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    • 제45권4호
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    • pp.896-901
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    • 1998
  • Pulmonary arteriovenous malformation(PAVM) is an uncommon congenital anomaly. As pulmonary arteriovenous malformation is a direct communication between the branches of pulmonary artery and vein which originated from the malformation of capillary development, major disturbances in gas exchange can result. This malformation results in the several symptoms such as dyspnea, hemopyssis, cyanosis, and severe neurologic complaints. However, the most of patients are usually asymptomatic. Selective pulmonary angiography is well known the helpful diagnostic method. Recently, therapeutic embolization has been advocated as the treatment of choice for pulmonary arteriovenous malformations. We report a case of multiple pulmonary arteriovenous malformation, which was detected on the simple chest X-ray and successfully treated with coil embolization in a 19-year-old asymptomatic woman.

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소아 환아의 경골 내에 발생한 동정맥 기형 - 1예 보고 - (Intraosseous Arteriovenous Malformation in a Pediatric Patient - A Case Report -)

  • 박수성;이종석;윤현기;정호욱
    • 대한골관절종양학회지
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    • 제14권1호
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    • pp.56-61
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    • 2008
  • 보고된 반 이상의 선천성 동정맥 기형이 사지에 발생한다. 그러나 주로 연부 조직에 발생하며 골 내에 생기는 경우는 적어 이에 대한 연구가 드물다. 또한 복잡하고 다양한 임상양상 때문에 진단 및 치료가 어려운 것으로 알려져 있다. 20개월 된 소아 여자 환자가 좌측 하지의 외상 없이 발생한 박동성 종괴를 주소로 내원하였다. 저자들은 경골 내에 발생한 동정맥 기형을 경험하고 에탄올 주입을 이용한 색전술로 좋은 결과를 얻었기에 문헌고찰과 함께 보고하는 바이다.

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폐동정맥루 (Pulmonary Arteriovenous Fistula -One Case Report-)

  • 최영호
    • Journal of Chest Surgery
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    • 제15권2호
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    • pp.183-187
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    • 1982
  • Pulmonary arteriovenous fistula is a congenital vascular malformation In the lung, various synonyms including Pulmonary cavernous vascular malformation, Pulmonary arteriovenous aneurysm, Cavernous hemangioma of the lung0 Pulmonary telangiectasia, Pulmonary hamartoma, etc. The pathogenesis of its symptoms is that unoxygenated, desaturated arterial blood enters into the pulmonary venous system directly. Recently we have experienced one case of the pulmonary arteriovenous fistula which was diagnosed as the pulmonary cystic lesion of the lung preoperatively in 20 years old, 61 kg, male patient. Operation was revealed well circumscribed cystic lesion filled with blood, subpleural and anterior mediobasal location, and bright red colored aspirates on two times needle aspirations. Microscopic finding shows ill circumscribed vascular lesion composed of varying sized blood vessels with irregular thickening of wall and final pathological diagnosis is Pulmonary Arteriovenous Fistula. Basal segmentectomy was done and the patient shows good postoperative course.

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Fontan Revision with Y-Graft in a Patient with Unilateral Pulmonary Arteriovenous Malformation

  • Lee, Jeong-woo;Park, Jeong-Jun;Goo, Hyun Woo;Ko, Jae Kon
    • Journal of Chest Surgery
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    • 제50권3호
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    • pp.207-210
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    • 2017
  • The extracardiac conduit Fontan procedure is the last surgical step in the treatment of patients with a functional single ventricle. An acquired pulmonary arteriovenous malformation may appear perioperatively or postoperatively due to an uneven hepatic flow distribution. Here we report a case of a bifurcated Y-graft Fontan operation in a 15-year-old male patient with a unilateral pulmonary arteriovenous malformation after an extracardiac conduit Fontan operation.

폐 동정맥루[치험 1례] (Pulmonary Arteriovenous Fistula - A Case Report -)

  • 정신현
    • Journal of Chest Surgery
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    • 제25권3호
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    • pp.315-320
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    • 1992
  • Pulmonary arteriovenous fistula is a rare congenital vascular malformation resulting from abnormal capillary development with incomplete formation of vascular septum normally dividing the primitive connections between the venous and arterial plexuses. Recently we have experienced a case of the bilateral pulmonary arteriovenous fistula in 7 years-old female patient. On admission, clinical manifestations were cyanosis of lips, clubbing and cyanosis of digits, and exertional dyspnea. The PO2 in arterial blood gas analysis was 43.3mmHg. In left upper and right lower lobe pulmonary arteriovenous fistulas were confirmed by bilateral pulmonary angiography. Left upper lobectomy and wedge resection of right lower lobe were performed respectively. Postoperative results were good.

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Pulmonary Arteriovenous Malformation and Its Vascular Mimickers

  • Hyoung Nam Lee;Dongho Hyun
    • Korean Journal of Radiology
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    • 제23권2호
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    • pp.202-217
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    • 2022
  • Pulmonary arteriovenous malformation (AVM) is a congenital vascular disease in which interventional radiologists can play both diagnostic and therapeutic roles in patient management. The diagnosis of pulmonary AVM is simple and can usually be made based on CT images. Endovascular treatment, that is, selective embolization of the pulmonary artery feeding the nidus of the pulmonary AVM, and/or selectively either the nidus or draining vein, has become a first-line treatment with advances in interventional devices. However, some vascular diseases can simulate pulmonary AVMs on CT and pulmonary angiography. This subset can confuse interventional radiologists and referring physicians. Vascular mimickers of pulmonary AVM have not been widely known and described in detail in the literature, although some of these require surgical correction, while others require regular follow-up. This article reviews the clinical and radiologic features of pulmonary AVMs and their mimickers.

구강악안면 영역에서의 동정맥 기형 치험례 (ARTERIOVENOUS MALFORMATION IN ORAL & MAXILLOFACIAL REGION : A CASE REPORT)

  • 김나영;김기홍;김성곤;이정구;조병욱
    • Journal of the Korean Association of Oral and Maxillofacial Surgeons
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    • 제28권1호
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    • pp.61-63
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    • 2002
  • 동정맥 기형은 혈관계의 형성, 성숙 동안에 발생되는 이상을 일컷는 일반적인 용어로서 현재 주로 혈관 전색술로 치료를 하고 있으나 불행하게도 항상 만족스러운 결과를 가져오지는 않는다. 또한 혈관 전색술에 도움이 되는 새로운 테크닉이 계속 개발되고 있으며 특히 외과의와 혈관 방사선 전문의와의 밀접한 협조 관계 및 주기적인 경과 관찰이 요구된다.