• Journal of the Korean Association of Oral and Maxillofacial Surgeons
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• 제43권4호
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• pp.267-271
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• 2017

Although it is a rare developmental malformation, van der Woude syndrome is the most common form of syndromic orofacial clefting, accounting for approximately 2% of all cleft cases. The lower lip pits with or without a cleft lip or palate is characteristic of the syndrome. Findings, such as hypodontia, limb deformities, popliteal webs, ankylogossia, ankyloblepheron, and genitourinary and cardiovascular abnormalities, are rarely associated with the syndrome. This paper reports a rare case of van der Woude syndrome in a 10-year-old male patient with a single median lower lip pit and a repaired bilateral cleft lip and cleft palate that were associated with microstomia, hypodontia, and clubbing of the left foot with syndactyly of the second to fifth lesser toes of the same foot.

• 대한치과교정학회지
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• 제31권1호
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• pp.63-69
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• 2001

구순열 및 구개열은 두개 악안면 부위에서 가장 자주 발생되는 선천성 기형으로 적절한 의료진의 확보와 의료 정책의 수립을 위해서 정착한 환자 수를 파악하는 것이 필요하다. 그러나, 기존의 국내 발생률 추정 연구는 표본선정의 문제점과 이 질환이 갖는 높은 유산율과 사산율 및 다양한 형태로 인한 분류의 어려움과 한국 내에서의 특수성 중 하나인 장애아들의 해외 입양으로 인해 정확한 환자 수의 파악이 어려웠다. 따라서, 한국인에서의 체계적인 유병률 연구가 필요하리라 사료되며, 대부분의 구순열 및 구개열 환자에서 필요한 교정 치료의 수혜 정도를 파악할 필요성이 있다고 사료된다. 이에 본 연구에서는 한국 성인 남자에서 구순열 및 구개열 환자에 대한 유병률과 이들에 대한 교정치료 수혜율을 조사하고자, 1998년도 병무청 징병 검사자 중 1979년도에 출생한 자만을 연구대상으로 하여 서울, 광주, 대구 부산의 성인 남자 218,322명에 대해 3단계 검사를 실시한 후 다음과 같은 결과를 얻었다. 1. 1979년 생 한국 성인남자에서 구순열 및 구개열 환자의 유병률은 1000명당 0.65명이었다. 2. 전후방적 심도에 따라 1000명당 각각의 유병률은 구순열이 0.26명, 구순구개열이 0.36명,구개열이 0.03명이었다. 구순열과 구순구개열은 비슷한 정도의 유병률을 보였으나, 구개열은 이에 비해 낮은 유병률을 보였다. 3. 횡적 심도에 따라 1000명당 각각의 유병률은 좌측 파열이 0.35명, 우측 파열이 0.16명, 양측 파열이 0.12명이었다. 좌측 파열은 우측 파열에 비해 매우 뚜렷하게 높은 유병률을 보였으며, 양측 파열은 편측 파열에 비해 낮게 나타났다. 4. 구순열 및 구개열 환자 중 성인남자에서의 한국 내 교정치료 수혜율은 $35\%$였으며, 구순열, 구개열, 구순구개열의 순으로 $28\%,\;29\%\;67\%$였다. 구순열이나 구개열과 같이 단독 발생된 경우보다 파열의 심도가 심한 구순구개열의 경우에서 교정치료 수혜율이 높게 나타났다.

• 대한구순구개열학회:학술대회논문집
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• 대한구순구개열학회 2003년도 종합학술대회
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• pp.30-30
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• 2003

• 대한치과교정학회지
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• 제23권3호
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• pp.319-326
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• 1993

The purpose of this study was to evaluate the frequency of congenital missing teeth and supernumerary teeth in cleft patients. The subjects were divided into bilateral cleft lip and palate(BCLP), unilateral cleft lip and palate(UCLP) and cleft palate alone(CP alone) groups. 97 cleft patients(BCLP 15, UCLP 70, CP alone 12) between 6-20 years old were evaluated. Panorama film, Orthodontic chart and initial intraoral photogram were employed for this research. The obtained results were as follows. 1. The incidence of congenital missing teeth in total cleft samples was $57.7\%$, and the incidence of supernumerary teeth was $26.8\%$. Each incidence was higher than non-cleft. 2. The incidence of congenital missing teeth was the highest in BCLP and the lowest in CP alone. 3. The number of congenital missing teeth per perso was usually one, and the frequency was higher in the maxillary lateral incisors$(67.8\%)$, and maxillary second premolar$(14.9\%)$ than other teeth. 4. Most of tooth number anomalies in cleft patients were found in maxilla, especially adjacent region to the cleft site.

• 대한구순구개열학회지
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• 제16권1호
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• pp.9-18
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• 2013

Distraction osteogenesis is useful treatment which the gradual separation of cut bone edges results in the generation of new bone. It is effective treatment for correcting maxillofacial deformities. Patients with cleft lip and palate usually have maxillary hypoplasia due to scarring of lip and palate. To correct these deformities, we chose to use a 2-jaw orthognathic surgery or distraction osteogenesis. But despite improvements in surgical techniques for maxillofacial deformities, postoperative stability still leaves the question of when relapse may occur. This case report describes the Relapse after treatment of maxillary hypoplasia with cleft lip and palate by Rigid External distraction system over a 2-year treatment and follow-up period. In addition, we reviewed related articles about the influence of the occlusal stability on postoperative stability in patients with cleft lip and palate correction with Distraction osteogenesis.

• 대한구순구개열학회지
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• 제10권1호
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• pp.39-56
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• 2007

The bilateral cleft lip, a more severe form of clefting than unilateral cleft lip, involves separation of the lip along philtral lines, isolating the central segment (prolabium). Bilateral cleft lip may be either symmetrical or asymmetrical, in which case the cleft lip is split more on one side than on the other. The cleft affects the obvious facial form as an anatomic deformity and has functional consequences, affecting the child's ability to eat, speak, hear, and breathe. Although there would seem to be quite a variance in reported figures, ratios of cleft lip with or without cleft palate have gone as high as 1:500 and as low as 1:1000. It is known that less than 10% of cleft lips are bilateral. Although bilateral cleft lip is less common than unilateral cleft lip, the deformity is more severe, and the reconstructive technique is more complex. Surgery is the only treatment necessary for patients with bilateral cleft lip. Accompanying the evolution of surgical repair is the increasingly important role of orthodontic support with early presurgical alveolar and nasal molding. Repositioning the maxillary and alveolar segments into a more anatomic position allows the surgeon to repair the lip and associated nasal deformity under more optimal conditions. The purpose of this article is to review the related anatomy, presurgical management, and surgical management of bilateral cleft lip.

• 대한구순구개열학회:학술대회논문집
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• 대한구순구개열학회 1997년도 종합학술대회
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• pp.38-38
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• 1997

• 대한구순구개열학회지
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• 제4권2호
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• pp.9-18
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• 2001

구순구개열은 악안면 영역의 선천기형 중 발생빈도가 가장 높으며 출생시부터 성장완료 시기까지 일관된 치료계획에 의한 종합적 진료체계가 필수적이다. 구순구개열의 개선을 위한 구개부 및 입숭? 조기 봉합 후의 반흔조직의 형성은 치열궁 협착 뿐 아니라 상악골 열성장에 의한 중안모의 함몰을 야기하며 이러한 상악골의 열성장 경향은 연령이 증가할수록 점진적으로 증가하는 성향을 보인다. 따라서, 성장잠재력을 이용한 조기의 악정형치료는 구순구개열 환자에서 반드시 필요하며, 적절한 치료 결과를 얻어내기 위하여 환자의 전후방 골격 형태 뿐 아니라, 성장 방향에 대한 고려가 필요하다. 그러나 혼합치열기의 악정형치료는 좋은 결과를 얻었다 하더라도 높은 재발 성향 및 잔여성장에 의한 악골관계의 변화가 예상되므로 장기간의 보정이 필수적이며 성장에 대한 지속적 평가가 이루어져야 할 것이다.

• 대한구순구개열학회지
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• 제12권1호
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• pp.7-20
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• 2009

Orthodontic treatment planning of cleft lip and palate requires consideration of the characteristic features, growth pattern and functional disorders related to cleft lip and palate patients. Tissue deficiencies and constriction of the scar tissue in surgically treated cleft lip and palate results in disturbance of maxillary growth and deficiency of midfacial region with anterior and posterior crossbite. These patients often present congenital missing of teeth, supernumerary teeth, malformed teeth, or ectopic position of teeth, which should be treated by orthodontic treatment by expanding upper arch followed by fixed appliance. Proper use of retainer and continuous follow-up is needed to prevent relapse after orthodontic treatment has finished. Also we have to pay attention to correct speech disorder which is caused by the velopharyngeal insufficiency.

• Maxillofacial Plastic and Reconstructive Surgery
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• 제19권3호
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• pp.260-264
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• 1997

The congenital deformities of cleft lip and cleft palate have been known to afflict man since prehistoric time. Efforts to correct these abnormities have evolved over the centuries as scientific knowledge has advanced. Although there is no agreement as to when the surgery should be performed, most surgeons adhere to "rule of 10" : the infant must be 10 week old weigh 10 Ibs, have a hemoglobin value 10gm/dl and have a white blood cell count no greater than 10 $thousands/mm^3$. Consensus favors performing initial palatal surgery in the child when he is between 18 and 24 months old. The timing of cleft alveolus surgery is usually between 10 and 11 years old. In the period from 1992 to 1996, 38 patients with cleft lip and cleft palate treated at the department of oral and maxillofacial surgery, Chosun university, dental hospital were analysed clinically. The obtained results were as follows. 1. The ratio of male to female was 1.92 : 1 (25/23) 2. The ratio of cleft lip, cleft palate and cleft lip & palate was 1.5 : 1 : 2.5 (12/8/18) 3. The ratio of unilateral to bilateral cleft lip was 5 : 1 (25/5) 4. The ratio of left to right side in unilateral cleft lip was 1.5 : 1 (15/10)