• 제목/요약/키워드: Chonnam

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장기간 인터페론 감마로 치료한 골화석증 2례 (Long-term recombinant interferon-γ treatment in 2 cases of osteopetrosis)

  • 김동연;한동균;백희조;정성택;국훈
    • Clinical and Experimental Pediatrics
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    • 제50권11호
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    • pp.1129-1133
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    • 2007
  • 골화석증은 뼈파괴세포의 기능의 이상과 백혈구의 과산화물 생성 이상을 특징으로 하는 드문 골경화성 질환으로, 유전방법이나 발병나이, 증상, 증상의 정도 등에 따라 몇 가지 아형으로 분류된다. 악성형 골화석증의 궁극적 치료 방법은 조혈모세포이식이지만, 조직형 일치 공여자가 없는 경우나 비교적 양성인 만성형 골화석증에서는 스테로이드나 carcitriol, 인터페론 감마 등의 치료를 시도해 볼 수 있다. 특히 인터페론 감마 치료는 골흡수를 증가시키고, 조혈 기능과 백혈구 기능을 향상시킨다고 보고되고 있다. 본 저자들은 약 6년, 3년 동안 인터페론 감마 치료 후 각각 수혈, 골절과 같은 다른 합병증 없이 조절되고 있는 골화석증 2례에 대해 보고하는 바이다.

Bronchiolitis Interstitial Pneumonitis 1예 (A Case of Bronchiolitis Interstitial Pneumonitis)

  • 지수영;유경호;임대훈;신홍준;반희정;오인재;권용수;김규식;임성철;김영철;최유덕;송상윤;선현주
    • Tuberculosis and Respiratory Diseases
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    • 제67권4호
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    • pp.364-368
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    • 2009
  • Bronchiolitis interstitial pneumonitis (BIP), an unclassified and newly described interstitial pneumonia, has a combined feature of prominent bronchiolitis, interstitial inflammation, and fibrosis. It is distinct from bronchiolitis obliterans or bronchiolitis obliterans organizing pneumonia (BOOP). BIP has a better prognosis than common cases of interstitial pneumonia. However, BIP has a poorer prognosis than BOOP. BIP's response to corticosteroids is not as successful as BOOP's response to this treatment. We encountered the case of a 31-year-old woman with BIP with an initial presentation of dyspnea and a cough that had lasted for 3 months. The patient's chest CT scan demonstrated patchy ground glass opacities and multiple ill-defined centrilobular nodules in both lungs, suggesting military tuberculosis or nontuberculous mycobacterial infection. A video-assisted thoracoscopic lung biopsy resulted in the diagnosis of BIP. Clinical symptoms, pulmonary lesions, and pulmonary function tests were improved after oral glucocorticoid therapy.

기관지동맥 색전술후 발생한 피질맹 1례 (Transient Cortical Blindness : A Rare Complication of Bronchial Artery Embolization)

  • 오인재;김규식;김수옥;이연경;주진영;조계중;박경화;고영춘;임성철;김영철;박경옥;윤웅;김재규
    • Tuberculosis and Respiratory Diseases
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    • 제53권2호
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    • pp.209-215
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    • 2002
  • 중증의 객혈에 대한 치료로써 기관지동맥 색전술을 시행한 후 일시적인 양측 시력 상실이 관찰되었으나 2-3일이 지나면서 점차적으로 호전되었다. 이는 혈관조영술상 보이지 않는 우좌단락을 통한 색전성 뇌허혈 또는 조영제의 신경독성에 의한 후두엽 손상으로 발생된 일시적인 피질맹으로써, 보존적인 치료 후 호전되었기에 문헌고찰과 함께 보고한다.

대상포진 후 발생한 비대흉터에 동반된 만성 통증 -증례 보고- (Hypertrophic Scar with Chronic Pain after Acute Herpes Zoster -A case report-)

  • 최종철;배홍범;정성태;김석재;정성욱;윤명하;정성수;유경연;정창영;최정일
    • The Korean Journal of Pain
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    • 제18권2호
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    • pp.229-231
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    • 2005
  • The most common and cumbersome complication of herpes zoster is postherpetic neuralgia, which typically presents as neuropathic pain. However, the painful symptoms of the postherpetic period might be associated with other causes, such as skin lesions of the herpes zoster. We report a case of a hypertrophic scar that developed in the lesion of an acute herpes zoster patient and was accompanied by pain.

Lung torsion after tracheoesophageal fistula repair in an infant

  • Yang, Eun Mi;Song, Eun Song;Jang, Hae In;Jeong, In Seok;Choi, Young Youn
    • Clinical and Experimental Pediatrics
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    • 제56권4호
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    • pp.186-190
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    • 2013
  • Lung torsion is a very rare event that has been reported in only 9 cases in the pediatric literature but has not yet been reported in Korean infants. We present a case of lung torsion after tracheoesophageal fistula repair in an infant. Bloody secretion from the endotracheal tube and chest radiographs and computed tomographic scan results indicated lung torsion. Emergency exploration indicated $180^{\circ}$ torsion of the right upper lobe (RUL) and right middle lobe (RML). After detorsion of both lobes, some improvement in the RUL color was observed, but the color change in the RML could not be determined. Although viability of the RML could not be proven, pexy was performed for both the lobes. Despite reoperation, clinical signs and symptoms did not improve. The bronchoscopy revealed a patent airway in the RUL but not in the RML. Finally, the RML was surgically removed. The patient was discharged on the 42nd day after birth.

Epithelioid Hemangioendothelioma Arising from Interanl Jugular Vein Mimicking Cervical Metastatic Lymphadenopathy

  • Yun, Ju Sik;Kang, Seung Ku;Kim, Sang Hyung;Na, Kook Joo;Song, Sang Yun
    • Journal of Chest Surgery
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    • 제48권4호
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    • pp.294-297
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    • 2015
  • Epithelioid hemangioendothelioma (EHE) is a relatively rare and moderately aggressive type of vascular tumor. We describe a case of EHE that presented in a 24-year-old woman as a palpable nodule in the left cervical area. Radiological examinations and fine-needle aspiration cytology led to a preliminary diagnosis of metastatic lymphadenopathy with an unknown primary site. However, during surgery, we determined that the nodule was an intra-vascular tumor arising from the left internal jugular vein. The histopathological examination revealed cords of epithelioid endothelial cells distributed in a hyaline stroma, compatible with a diagnosis of EHE.

Transvenous proximal closure of large congenital coronary arteriovenous fistula using the single Amplatzer vascular plug in a 3-year-old girl

  • Jang, Hae In;Choi, Young Earl;Cho, Hwa Jin;Cho, Young Kuk;Ma, Jae Sook
    • Clinical and Experimental Pediatrics
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    • 제56권2호
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    • pp.90-93
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    • 2013
  • Congenital coronary arteriovenous fistulas (CCAFs) are rare coronary artery abnormalities in which blood is shunted into a cardiac chamber or great vessel. If the fistula itself is large and tortuous, it is generally recommended to occlude the fistula to prevent several complications. In approaches of transcatheter occlusion, the transvenous approach is preferred over the transarterial approach. The transvenous approach would enable the cannulation of a relatively larger catheter or sheath without potential damage to the femoral vessels or normal coronary arteries, which can occur in the transarterial approach. The transvenous approach may also minimize the blind pouch after releasing the devices. Herein, we report the success of transvenous proximal closure of a CCAF using an Amplatzer vascular plug (AVP) in a 3-year-old patient with cardiomegaly. Complete occlusion was achieved by a single AVP and thrombus formation of the distal aneurysmal portion of the fistula. We suggest that this strategy of closing the proximal end with a dilated fistula using a single AVP by the transvenous approach may be a good option in treating CCAFs in a young child.

삼상 뼈스캔으로 진단된 소아기 피부근육염 (Juvenile Dermatomyositis Diagnosed by $^{99m}Tc$-HDP Three-phase Bone Scintigraphy)

  • 김자혜;송호천;유수웅;하정민;정아리;오종률;민정준;범희승;정은희;이민철
    • Nuclear Medicine and Molecular Imaging
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    • 제43권6호
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    • pp.592-595
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    • 2009
  • Juvenile dermatomyositis is a common inflammatory muscle disease of childhood, characterized by weakness in proximal muscles and specific skin rash. In case of juvenile dermatomyositis without characteristic clinical features, non-invasive imaging tools such as $^{99m}Tc$-HDP three-phase bone scan are very helpful in diagnostic workup of myopathies. We report a case of 13-year old female with juvenile dermatomyositis, in which $^{99m}Tc$-HDP three-phase bone scan was useful in diagnosis and assessing therapy response.