• Archives of Plastic Surgery
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• 제35권1호
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• pp.104-106
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• 2008

Purpose: Fewer than 100 cases of calcifying aponeurotic fibroma have been reported in the literature since this entity was initially described by Keasbey in 1953 who called it calcifying juvenile aponeurotic fibroma. The tumor is a slowly growing, painless mass. In most cases the mass is poorly circumscribed and causes neither discomfort nor limitation of movement. Most lesions occur in children, with a peak incidence ages of 8-14 years. There is no evidence of any increased familial prevalence. Predilection sites are palm, finger, toe, but it also occurs in the wrist, forearm, elbow, upper arm, neck, abdominal wall, lumbar paravertebral area, leg and ankle. We herein describe a rare case of calcifying aponeurotic fibroma occurring on the chin with review of the literature. Methods: A 14-year-old male had painless, slowly growing mass(${\phi}2.5cm$) on a chin for a year. The tumor was excised elliptically under local anesthesia and the excisional site was repaired directly. Due pathological examination was processed. Results: Histological examination revealed an illdefined fibrous growth that extends with multiple processes into the surrounding tissue with centrally located foci of calcification. The tumor is composed of short spindled plump fibroblasts with round or ovoid nuclei separated by collagenous stroma, showing vaguely palisading pattern. Diagnosis of calcifying aponeurotic fibroma was conferred. Postoperatively, the patient did well, and the lesion had not recurred. Conclusion: Fewer than 100 cases of calcifying aponeurotic fibroma have been reported in the literature. The most common occurring sites are palm, finger & toe, but it has been reported in the wrist, forearm, elbow, upper arm, neck, abdominal wall, lumbar paravertebral area, leg and ankle. Two cases of calcifying aponeurotic fibroma occurring on the neck have been reported in the literature. To the authors knowledge, our case of calcifying aponeurotic fibroma occurring on the chin is the first to be reported.

• Maxillofacial Plastic and Reconstructive Surgery
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• 제17권2호
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• pp.195-201
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• 1995

This is a case report of calcifying aponeurotic fibroma occurred in the right pterygopalatine fossa & ramus area accompanied by adenoid cystic carcinoma of the right sublingual gland of a 44-year-old female. Calcifying aponeurotic fibroma is benign tumor, but it is characterized by poorly marginated, infiltrated growth pattern and a stubborn tendency to local recurrence, but there is no record of malignant transformation or metastasis, and surgical management should be conservative(excision and reexcision). Most cases been reported at the hands and feet, but no reported case occuring in the head region is found in the literature. Adenoid cystic carcinoma is a slow-growing infiltrative tumor with high recurrence rate, and it's treatment requires radical excisin and radiotherapy. Wide surgical excision of tumor, RND and partial resection of mandible were done. And then, immediate mandibular reconstruction was performed by means of reimplantaion technique after autoclaving of the resected bone.

• Journal of Yeungnam Medical Science
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• 제20권2호
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• pp.223-228
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• 2003

석회화건막섬유종은 매우 드문 양성 연부조직 종양으로 소아와 청소년기에 팔다리, 특히 손과 발에 발생한다. 저자들은 오른쪽 엄지손가락에 발생한 석회화건막섬유종 1예를 경험하였기에 문헌 고찰과 함께 보고한다. 14세 남자가 오른쪽 엄지손가락의 종괴를 주소로 내원하였다. 방사선 소견에서 연부조직 병변이 오른쪽 엄지손가락의 손허리손가락관절 부위에 관찰되었다. 종괴에 대한 절제가 시행되었다. 절제된 종괴는 $2.0{\times}1.5cm$ 크기의 회백색을 띠는 섬유성 조직이었다. 조직학적으로 종괴는 섬유모세포의 증식과 주위조직으로 침윤성 성장을 보였다. 종괴 내부에 부분적인 석회화와 연골 분화가 관찰되었다.

• Journal of Oral Medicine and Pain
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• 제44권1호
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• pp.35-39
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• 2019

Calcifying aponeurotic fibroma (CAF) is an uncommon benign soft-tissue fibroblastic tumor with characteristic histological features. It mainly occurs in the distal part of the extremities, such as the hands and feet, in children and adolescents. Males are twice as commonly affected as females. CAF exhibits local invasiveness, and hence, its recurrence rate is also high. Therefore, complete surgical excision is both diagnostic and therapeutic. The occurrence of CAF in the maxillofacial region, especially the temporomandibular joint (TMJ), is very rare, and this necessitates its differentiation from other TMJ neoplasms. The differential diagnosis of CAF requires microscopic examination. Herein, we report a rare case of CAF located at the left mandibular condyle, which was confirmed by histopathological analysis.

• Investigative Magnetic Resonance Imaging
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• 제21권4호
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• pp.259-263
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• 2017

Calcifying aponeurotic fibroma (CAF) is an uncommon benign tumor and a locally aggressive fibroblastic lesion. It commonly affects the palmar side of the hand and fingers, and the soles of the feet. The typical clinical manifestations are known as a poorly circumscribed, slow-growing, and asymptomatic firm mass. Most CAFs usually reveal low to intermediate or isointensity on T1-weighted images, and strong heterogeneous enhancement. However, various signal intensities on T2-weighted images have been reported depending on the degree of hypocellularity or the amount of calcification or collagen within the tumor. This report provides the radiographic and MRI finding of CAF arising in uncommon site, the knee region, of a 19-year-old male who presented with a painful and palpable mass.

• 대한골관절종양학회지
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• 제9권2호
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• pp.233-237
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• 2003

목적: 석회화 건막 섬유종은 소아 및 청소년층에서 수장부를 가장 많이 침범하는 양성이나 공격적 성향을 띈 섬유성 종양이다. 저자들은 최근에 15세 소년의 수부에 발생한 석회화 건막 섬유종의 치료를 경험하였기에 이를 문헌 고찰과 함께 보고하고자 한다. 증례: 15세 소년이 좌수의 소지구 부위에 재발하는 종물을 주소로 내원하였으며 이 소년은 7년전에 타 병원에서 국소 마취 하에 동일 부위에 발생한 종물을 제거한 기왕력을 가지고 있었다. 종물은 단단하였으며 압통이 있었다. 단순 방사선 촬영상에는 종물 내에 다소성으로 산재된 미세 석회 침착이 보였다. 수술 소견상 종물은 주변과 명확히 구분되지 않았으며 단단하고 옅은 회색빛의 석회화를 동반한 침습성의 결절성 형태를 보였으며 가이언 관내의 척골 신경과 척골 동맥이 바로 인접하고 있었다. 수술 후 제거한 종물을 현미경적으로 관찰한 결과 종물은 많은 석회 침착이 되어 있으면서 이형성 연골양 분화를 보이는 조직이 중간 중간에 섞여 있는 빽빽한 섬유 조직의 증식으로 이루어져 있었고 주변부는 명확히 경계 지어지지 않으며 분엽상을 보이고 있었다. 결론: 이 질환에 있어서 가장 바람직한 치료법은 기능적인 면과 주요 조직을 보존할 수 있는 한도내에서 광범위 절제를 시행하는 것이며 이렇게 치료하더라도 많게는 50 %이상의 재발율이 보고되고 있는 실정이다.