• 제목/요약/키워드: Associated anomalies

검색결과 412건 처리시간 0.027초

대동맥 교약증의 수술요법 -12년간의 수술경험- (Surgical Management of Coarctation of the Aorta: 12 Years of Experience)

  • 김원곤;서경필
    • Journal of Chest Surgery
    • /
    • 제18권1호
    • /
    • pp.36-45
    • /
    • 1985
  • During the twelve-year period from March 1973 through July 1984, 23 consecutive operations for coarctation of the aorta were performed at Seoul National University Hospital. The patients included 19 male and 4 female in the range of 4 months and 16 years old. Associated cardiac anomalies were present in 19 patients [70%] and they were VSD+PDA [9 patients], VSD[2], PDA[1], VSD+ASD+PDA[1], VSD+MS+AS+PDA[1], D-TGA+VSD+PDA[1], P-ECD[1], MS[1], Al[1], and DORV+PDA[1]. The preoperative main symptoms included congestive heat failure, hypertension, subacute bacterial endocarditis and nonspecific symptoms. Congestive heart failure was the most common symptom in the group younger than 2 years and hypertension in the adult group. Operative techniques for coarctation of the aorta were resection and end to end anastomosis in 10 patients, prosthetic patch aortoplasty in 8, subclavian flap aortoplasty in 4, and LSCA-aortic anastomosis in 1. There were 4 operative deaths among the nine patients less than 2 years old[44.4% mortality]: all of these patients had associated cardiac anomalies. And only one operative death occurred in patients older then 2 years old[7.1% mortality]. No hospital death occurred in patients with isolated coarctation of the aorta. Operation of the coarctation was performed primarily in 6 patients associated with ventricular septal defect and subsequently underwent successful VSD closure except one operative death.

  • PDF

대동맥판막하 막상협착증의 수술요법 (Surgical Treatment of Discrete Subaortic Stenosis)

  • 노준량;이재원
    • Journal of Chest Surgery
    • /
    • 제19권1호
    • /
    • pp.165-173
    • /
    • 1986
  • During the 4 year period from 1982 through 1985, twelve patients have undergone operations for discrete subaortic stenosis with good short-term clinical result at Department of Thoracic and cardiovascular Surgery, S.N.U.H. According to the cineangiographic and operative findings, nine of the 12 patients were classified as Deutsch type I, the other 3 as type II, and eleven of the 12 had one or more associated anomalies of the cardiovascular system such as PDA[5], VSD[5], left SVC[2], MS[1], COA[1], supramitral membrane[1], DORY[1], right aortic arch[1], DCRV[1], and TOF[1] [one with Shone`s complex], and three of them had secondary cardiac disorders such as aortic regurgitation[3],mitral regurgitation[2], and tunnel shaped dynamic obstruction of left ventricular outflow tract[2]. We have performed membrane resection via oblique aortotomy with retraction of the aortic cusps in 7 cases and via VSD from right cardiac chamber in 5 cases with large VSD and have also performed the operations on the correctable associated anomalies. There was only one operative death in patient with associated TOF due to neurologic complication and no other postoperative difficulties except in one patient with transient heart block resolved spontaneously on postoperative 3rd day. To our knowledge, this article is the first report of operation for discrete subaortic stenosis in Korean literature.

  • PDF

Associated Brain Parenchymal Abnormalities in Developmental Venous Anomalies: Evaluation with Susceptibility-weighted MR Imaging

  • Ryu, Hyeon Gyu;Choi, Dae Seob;Cho, Soo Bueum;Shin, Hwa Seon;Choi, Ho Cheol;Jeong, Boseul;Seo, Hyemin;Cho, Jae Min
    • Investigative Magnetic Resonance Imaging
    • /
    • 제19권3호
    • /
    • pp.146-152
    • /
    • 2015
  • Purpose: The purpose of this study was to evaluate the associated brain parenchymal abnormalities of developmental venous anomalies (DVA) with susceptibility-weighted image (SWI). Materials and Methods: Between January 2012 and June 2013, 2356 patients underwent brain MR examinations with contrast enhancement. We retrospectively reviewed their MR examinations and data were collected as per the following criteria: incidence, locations, and associated parenchymal signal abnormalities of DVAs on T2-weighted image, fluid-attenuated inversion recovery (FLAIR), and SWI. Contrast enhanced T1-weighted image was used to diagnose DVA. Results: Of the 2356 patients examined, 57 DVAs were detected in 57 patients (2.4%); 47 (82.4%) were in either lobe of the supratentorial brain, 9 (15.7%) were in the cerebellum, and 1 (1.7%) was in the pons. Of the 57 DVAs identified, 20 (35.1%) had associated parenchymal abnormalities in the drainage area. Among the 20 DVAs which had associated parenchymal abnormalities, 13 showed hemorrhagic foci on SWI, and 7 demonstrated only increased parenchymal signal abnormalities on T2-weighted and FLAIR images. In 5 of the 13 patients (38.5%) who had hemorrhagic foci, the hemorrhagic lesions were demonstrated only on SWI. Conclusion: The overall incidence of DVAs was 2.4%. Parenchymal abnormalities were associated with DVAs in 35.1% of the cases. On SWI, hemorrhage was detected in 22.8% of DVAs. Thus, we conclude that SWI might give a potential for understanding of the pathophysiology of parenchymal abnormalities in DVAs.

Outcomes of Surgical Treatment of Vascular Anomalies on the Vermilion

  • Park, Sang Min;Bae, Yong Chan;Lee, Jae Woo;Kim, Hoon Soo;Lee, In Sook
    • Archives of Plastic Surgery
    • /
    • 제43권1호
    • /
    • pp.19-25
    • /
    • 2016
  • Background The vermilion plays an important role in both the aesthetic and functional aspects of facial anatomy. Due to its structural features, the complete excision of vascular anomalies on the vermilion is challenging, making it difficult to determine the appropriate treatment strategy. Thus, the authors analyzed the results of surgical treatment of vascular anomalies on the vermilion. Methods The medical records of 38 patients with vascular anomalies on the vermilion who underwent surgery from 1995 to 2013 were analyzed. Nine of the cases had an involuted hemangioma, and 29 cases had a vascular malformation; of the vascular malformations, 13, 11, one, and four cases involved were capillary malformations (CMs), venous malformations (VMs), lymphatic malformations (LMs), and arteriovenous malformations (AVMs), respectively. We investigated the surgical methods used to treat these patients, the quantity of surgical procedures, complications and instances of recurrence, and self-assessed satisfaction scores. Results A total of 50 operations were carried out: 28 horizontal partial excisions, eight vertical partial excisions, and 14 operations using other surgical methods. All cases of AVM underwent complete excision. Six cases experienced minor complications and one case of recurrence was observed. The overall average satisfaction score was 4.1 out of 5, while the satisfaction scores associated with each lesion type were 4.2 for hemangiomas, 3.9 for CMs, 4.2 for VMs, 5.0 for LMs, and 4.0 for AVMs. Conclusions It is difficult to completely excise vascular anomalies that involve the vermilion. This study suggests that partial excision focused on correcting the overall contour of the lips is effective and leads to satisfactory results.

울릉분지에서의 선상중력과 위성중력 통합에 의한 중력 해상도 향상 및 해석 (High Resolution Gravity Mapping and Its Interpretation from both Shipborne and Satellite Gravity Data in the Ulleung Basin)

  • 박찬홍;김정우;허식;원중선;석봉출;유해수
    • 지구물리
    • /
    • 제2권1호
    • /
    • pp.27-38
    • /
    • 1999
  • 최근 공개된 위성중력을 이용하는 오차 최소화 기법을 적용하여 선상중력내 존재하는 구간 측선간 오차나 교차점 오차를 성공적으로 보정하였으며, 보정된 선상중력을 위성중력과 결합하여 고해상 중력분포를 도출하였다. 오차 최소화 과정에서 울릉분지의 선상중력은 위성중력보다 장주기 성분에서 상대적으로 크게 보정되었으나 단주기 성분은 그대로 보존되었다. 이것은 선상중력이 갖는 단주기의 중력 성분이 훼손되지 않은 채 안정되고 연속성을 갖는 장주기의 인공위성 중력분포에 잘 접합될 수 있다는 것을 보여 준다. 통합된 후리에어이상도는 위성중력의 장주기 성분과 선상중력의 단주기 성분을 모두 표현하므로 해저지형 및 지질분포의 해석에서 보다 상세하고 신뢰성 있는 정보를 제공한다. 후리에어이상은 수심이 깊은 분지 중앙 지역이 해저산이나 대지 등 높은 지형으로 이루어진 분지 주변부 보다 상대적으로 낮게 분포하는 등 전반적으로 해저지형의 분포 경향에 부합되어 변화한다. 그러나 대륙사면을 이루고 있는 분지의 서쪽 및 동쪽 주변부를 따라서는 지역적으로 함몰된 퇴적기반과 두꺼운 퇴적층 및 대륙 주변부에서 특징적인 가장자리 효과로 인한 저이상대가 발달하고 있다. 울릉도 북동부에 위치한 한국대지 및 울릉대지에서 북동-남서방향의 선형분포를 갖는 중력이상은 동해가 열개되는 동안 균열된 지각 사이를 따라 일어난 화산활동의 결과로 형성된 해산이나 관입암체가 선형으로 배열함으로서 기인한 것으로 해석된다. 선형으로 배열된 고중력분포는 울릉대지 서쪽 경계부에서 급구배를 보이는 북북서-남남동 방향의 직선적인 중력분포에 의해 절단되고 있는 데 이 급구배의 중력이상은 울릉대지 서부 경계를 이루는 단층선애에 기인한다. 울릉대지가 서쪽으로 뚜렷한 단층 접촉을 나타내고 있으나 지형적인 형태에 있어서 대비되지 않는 것은 울릉대지가 단층을 경계로 분리되어 이동되어 왔을 가능성을 시사한다. 분지의 중앙 북동부에서는 수심이 깊어지는 데 비해 중력치는 오히려 높아지는 경향을 나타내고 있는 것은 맨틀이 주변부에 비해서 상대적으로 천부에 존재하고 있는 것이 가장 큰 요인이며, 해저지각의 두께가 얇은 대신 지각의 밀도가 주변 대륙보다 높은 데도 기인한다.

  • PDF

한국의 춘계한발의 종관기후학적 특성 (Synoptic Climatological Characteristics of Spring Droughts in Korea)

  • 양진석
    • 한국지역지리학회지
    • /
    • 제4권1호
    • /
    • pp.43-56
    • /
    • 1998
  • 본 연구는 한국에 있어서 춘계한발시 기후요소의 분포특성과 지상기압장 및 500hPa등압면의 종관기후학적 특성을 평년과 비교분석한 연구이다. 춘계한발시 한국에 있어서의 일최저기온편차의 지역적 분포는 양의 편차역과 음의 편차역이 혼재하고 있으나 3월은 음의 편차역이 넓게 분포하여 한반도 주변에 서고동저형의 기압배치의 출현빈도가 높음을 반영하고 있다. 일최고기온은 양의 편차를 나타내어 강수일과 운량 및 습도가 감소하여 일사량이 많고 따라서 증발량이 증대됨을 나타낸다. 춘계 한발시 지상기압장의 기압편차가 3월은 한반도를 경계로 동쪽은 음의 편차 서쪽은 양의 전차를 나타내어 서고동저형의 기압배치의 출현빈도가 높고 5월은 한반도와 그 주변은 대상의 정편차역에 속하여 이동성 고기압의 출현빈도가 높음을 반영하고 있다. 500hPa등압면의 고도편차에서 3월은 지상기압장과 유사하게 한반도를 경계로 동쪽은 음의 편차 서쪽은 양의 편차역이 분포하며 4월은 3월과 유사하지만 음의 편차역이 서쪽으로 확장되어 있다. 5월은 한반도와 그 주변이 대상의 양의 편차역에 속하며 캄차카반도 주변 오호츠크 해상에 발달한 저지고기압(blocking high)이 지상 고기압의 동진을 지연시켜 이동성 고기압이 한반도주변에 장기간 정체됨을 나타낸다. 따라서 한발시에는 동서지수는 저지수를 나타내어 동서류가 약한 반면 한반도는 북태평양서안에 형성된 trough의 서쪽에 위치하여 건조한 북서기류의 유입이 빈번함을 나타내고 3원의 한발시에는 3 4월과는 다르게 동서지수가 고지수를 나타내어 건조한 동서류가 강할 때 한발이 출현하여 조춘의 한발시와 만춘의 한발시의 메카니즘이 상이함을 밝혔다.

  • PDF

선천성 낭포성 선양기종: 1례 보고 (Congenital Cystic Adenomatoid Malformation of The Lung - A Case Report -)

  • 김명인
    • Journal of Chest Surgery
    • /
    • 제24권8호
    • /
    • pp.819-823
    • /
    • 1991
  • The congenital cystic adenomatoid malformation of the lung is a rare disease, and is one of the most common congenital lung diseases which require prompt surgical intervention. The prognosis depends on its tissue type, prompt diagnosis and surgical intervention. The lesion consists of enlarged, variable sized multiple cyst with overgrowth of terminal bronchioles, like hamartoma. This disease can be associated with other vascular anomalies or other congenital defect especially in type II lesion We recently experienced one case of congenital cystic adenomatoid malformation The patient was 2 months old infant who showed respiratory distress without associated anomaly. After right upper lobe lobectomy, the patient was recovered uneventfully.

  • PDF

4첨 대동맥판막 환자에서 발생한 대동맥 판막폐쇄부전 -1례 보고- (Quadricuspid Aortic Valve Associated with Aortic Regurgitation -Report of A case-)

  • 박국양;김성철;김창호
    • Journal of Chest Surgery
    • /
    • 제23권3호
    • /
    • pp.527-531
    • /
    • 1990
  • A 11 year-old girl with quadricuspid aortic avlve associated with regurgitation left superior vena cava and chromosomal anomaly is presented. The quadricuspid valve was unexpectedly found during operation for aortic valve replacement. The aortic valve consisted of 4 equal-sized cusps and retrospective review of the aortogram revealed the aortic valve to have 4 cusps also. To the best of our knowledge, this combination of anomalies has not been reported in Korea previously.

  • PDF

Supramitral ring -1예 보고- (Supramitral Ring -1 Case Report-)

  • 이종욱
    • Journal of Chest Surgery
    • /
    • 제21권4호
    • /
    • pp.741-747
    • /
    • 1988
  • Supramitral ring is a very rare cardiac lesion which frequently associated other congenital anomalies of the heart and great vessels. We present a case of isolated supramitral stenosis ring of the left atrium without an associated lesion who have had operated in this hospital. He was 22 months old male and postoperative course was excellent. The importance of careful clinical examination, angiocardiography, echocardiography before operation is emphasized. Since this lesion is potentially curable by operation, repair with use of cardiopulmonary bypass should be performed without delay once the diagnosis has been made.

  • PDF

후장중복증을 동반한 변형 총배설강외반증 (A Cloacal Exstrophy Variant Associated with Hindgut Duplication)

  • 이태석;오수명
    • Advances in pediatric surgery
    • /
    • 제1권2호
    • /
    • pp.190-194
    • /
    • 1995
  • Diphallus is a rare congenital anomaly and is frequently associated with duplication of the urinary tract and rectosigmoid, and commonly associated with vertebral anomalies. Remzi reported less than 100 cases of duplication of all or a portion of the penis, but about 10 cases of complete diphallus with exstrophy of cloaca was reported, and a case of complete diphallus associated with hindgut duplication was reported, and complete diphallus with displacement of bladder associated hindgut duplication and imperforate anus was not reported in Korea. We experienced a case of the complete diphallus associated with displacement of bladder, hindgut duplication, and imperforate anus as a variant of cloacal exstrophy. A review of published cases suggests that this may be the first example of a complete diphallus with displacement of bladder coexisting with the hindgut duplication and imperforate anus.

  • PDF