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http://dx.doi.org/10.5090/kjtcs.2010.43.3.336

Spontaneous Hemothorax in a Patient with Type IV Ehlers-Danlos Syndrome - A case report -  

Han, Kook-Nam (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
Kim, Young-Tae (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
Nam, Jin-Hae (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
Choi, Jin-Ho (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
Kang, Chang-Hyun (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
Kim, Joo-Hyun (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
Publication Information
Journal of Chest Surgery / v.43, no.3, 2010 , pp. 336-339 More about this Journal
Abstract
We successfully performed bleeding control using roll-gauze packing in a patient with Type IV Ehlers-Danlos syndrome and this patient was suffering from spontaneous hemothorax. Thoracotomy for controlling ongoing bleeding in a patient with Type IV Ehlers-Danlos syndrome should be performed as a last resort after due consideration.
Keywords
Hemothorax; Ehlers-Danlos syndrome;
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1 Pepin M, Schwarze U, Superti FA, Byers PH. Clinical and genetic features of Ehlers-Danlos syndrome type IV, the vascular type. N Engl J Med 2000;342:673-80   DOI   ScienceOn
2 Paepe A. Ehlers-Danlos syndrome type IV. Clinical and molecular aspects and guidelines for diagnosis and management. Dermatology 1994;189(Suppl II):21-5   DOI
3 Kuivaniemi H, Tromp G, Prockop DJ. Mutations in fibrillar collagens (types I, II, III, and XI), fibril-associated collagen (type IX), and network-forming collagen (type X) cause a spectrum of diseases of bone, cartilage, and blood vessels. Hum Mutat 1997;9:300-15   DOI   ScienceOn
4 Caceres M, Buechter KJ, Tillou A, Shih JA, Liu D, Steeb G. Thoracic packing for uncontrolled bleeding in penetrating thoracic injuries. South Med J 2004;97:637-41   DOI   ScienceOn
5 Malfait F, Paepe A. Bleeding in the heritable connective tissue disorders: mechanisms, diagnosis and treatment. Blood Rev 2009;23:191-7   DOI   ScienceOn
6 Ali HA, Lippmann M, Mundathaje U, Khaleeq G. Spontaneous hemothorax: a comprehensive review. Chest 2008;134:1056-65   DOI   ScienceOn
7 Faber P, Craig WL, Duncan JL, Holliday K. The successful use of recombinant factor VIIa in a patient with vaszculartype Ehlers-Danlos syndrome. Acta Anaesthesiol Scand 2007;51:1277-9   PUBMED   ScienceOn
8 Dominguez J, Sancho C, Escalante E, Morera JR, Moya JA, Bernat R. Percutaneous treatment of a ruptured intercostal aneurysm presenting as massive hemothorax in a patient with type I neurofibromatosis. J Thorac Cardiovasc Surg 2002;124:1230-2   DOI   ScienceOn