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http://dx.doi.org/10.5125/jkaoms.2020.46.1.70

Osteogenesis imperfecta and combined orthodontics and orthognathic surgery: a case report on two siblings  

Kim, Dong-Young (Department of Oral and Maxillofacial Surgery, Asan Medical Center)
Baik, Unbong (Private Clinic)
Jeon, Ju-Hong (Department of Oral and Maxillofacial Surgery, Asan Medical Center)
Publication Information
Journal of the Korean Association of Oral and Maxillofacial Surgeons / v.46, no.1, 2020 , pp. 70-77 More about this Journal
Abstract
Osteogenesis imperfecta is a heterogeneous group of connective tissue diseases that is predominantly characterized by bone fragility and skeletal deformity. Two siblings with undiagnosed type I osteogenesis imperfecta underwent orthognathic surgery for the treatment of facial asymmetry and mandibular prognathism. The authors report two cases of combined orthodontics and orthognathic surgery in patients with type I osteogenesis imperfecta, mandibular prognathism, and facial asymmetry.
Keywords
Osteogenesis imperfecta; Orthognathic surgery;
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