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http://dx.doi.org/10.7181/acfs.2021.00185

Treatment of Morbihan disease  

Kim, Joo Hyoung (Department of Plastic and Reconstructive Surgery, Pusan National University School of Medicine and Biomedical Research Institute, Pusan National University Hospital)
Publication Information
Archives of Craniofacial Surgery / v.22, no.3, 2021 , pp. 131-134 More about this Journal
Abstract
Morbihan disease (MD) is a rare condition that involves rosaceous lymphedema or erythematous lymphedema of the middle and upper thirds of the face. It typically affects the periorbital region, forehead, glabella, nose, and cheeks. The etiology of MD remains unclear, and its diagnosis is challenging. MD often tends to be unresponsive to therapies commonly used to treat rosacea, including corticosteroids, isotretinoin, and antibiotics. Surgical treatments have therefore been attempted, but most cases showed unsatisfactory responses. These problems could have resulted from an incorrect recognition and interpretation of the pathophysiology of MD and inaccurate planning of the operation, resulting in recurrence or exacerbation of edema.
Keywords
Edema; Eyelids; Lymphedema;
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