대한두경부종양학회지 (Korean Journal of Head & Neck Oncology)

  • 제40권1호
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  • Pages.49-53
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  • 2024
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  • 1229-5183(pISSN)
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  • 2586-2553(eISSN)
대한두경부종양학회 (The Korean Society for Head and Neck Oncology)
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비전형적 임상양상을 보이는 후두부의 융기성 피부 섬유 육종에 대한 증례보고

Dermatofibrosarcoma Protuberans on the Occipital Scalp Showed Uncommon Presentation: A Case Report

  • 정지원 (한림대학교 강동성심병원 성형외과) ;
  • 정철훈 (한림대학교 강동성심병원 성형외과) ;
  • 조성진 (한림대학교 강동성심병원 병리과)
  • Jiwon Jeong (Department of Plastic and Reconstructive Surgery, Hallym University Kangdong Sacred Heart Hospital ) ;
  • Chul Hoon Chung (Department of Plastic and Reconstructive Surgery, Hallym University Kangdong Sacred Heart Hospital ) ;
  • SeongJin Cho (Department of Pathology, Hallym University Kangdong Sacred Heart Hospital)
  • 투고 : 2023.12.07
  • 심사 : 2024.01.24
  • 발행 : 2024.05.30
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초록

Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue sarcoma, with an incidence of about 0.8% to 5% per million people per year, accounting for 1% of soft tissue sarcomas. In its early stage, DFSP is typically found as a violet or pinkish macule or patch, and it can develop into a palpable mass with ulceration or bleeding. The standard treatment for DFSP is wide local excision of the tumor with a 2- to 3-cm negative margin, and radiation therapy or chemotherapy can be conducted with surgical treatment. A 35-year-old man had a palpable mass on the left side of his occipital scalp without color change, ulceration, or bleeding, which typically are present in malignancy. A magnetic resonance imaging (MRI) scan showed a 3-cm homogenous enhanced mass without adhesion between the scalp and the mass. Unexpectedly, a biopsy revealed the round mass to be DFSP. A wide excision and rotation of the scalp flap were performed. The patient recovered without any complications and received adjuvant radiotherapy at a dose of 60 Gray (Gy) for six weeks. There was no recurrence through six months of follow-up. Here we report this unique case of DFSP with atypical presentation.

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참고문헌

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