대한두개안면성형외과학회지 (Archives of Craniofacial Surgery)

  • 제24권4호
  • /
  • Pages.185-188
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  • 2023
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  • 2287-1152(pISSN)
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  • 2287-5603(eISSN)
대한두개안면성형외과학회 (Korean Cleft Palate-Craniofacial Association)
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Simultaneous diagnosis and resection of orofacial rhabdomyosarcoma with frozen section biopsy: a case report

  • Youngwoong Choi (Department of Plastic and Reconstructive Surgery, Inje University Ilsan Paik Hospital) ;
  • Ki Pyo Sung (Department of Plastic and Reconstructive Surgery, Inje University Ilsan Paik Hospital) ;
  • Soo Hyang Lee (Department of Plastic and Reconstructive Surgery, Inje University Ilsan Paik Hospital)
  • 투고 : 2023.02.24
  • 심사 : 2023.06.20
  • 발행 : 2023.08.20
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초록

Rhabdomyosarcoma is the most common soft tissue sarcoma in children, accounting for 4.5% of all cases of cancer in childhood. Although the head and neck are the most common sites of rhabdomyosarcoma, oral lesions are relatively rare and account for only 10% to 12% of head and neck rhabdomyosarcoma cases. This is a case report of a girl aged 2 years and 1 month who initially presented with an upper lip mass that invaded the oral mucosa, oral skin, and nostril skin, causing narrowing of the airway. Through our case, we show that rapidly growing small round cell malignancies, especially rhabdomyosarcoma, can be effectively diagnosed and treated at the same time using primary resection with intraoperative frozen section biopsy and that the time spent waiting for the results of preoperative biopsy can be saved in this way, particularly when the patient's symptoms are intensifying rapidly and require immediate operation.

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참고문헌

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