Annals of Hepato-Biliary-Pancreatic Surgery (한국간담췌외과학회지)

The Korean Association of Hepato-Biliary-Pancreatic Surgery (한국간담췌외과학회)
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Vascular tumors of the liver: A brief review

  • Sujata Sarangi (Department of Pathology, Grant Govt. Medical College) ;
  • Balamurugan Thirunavukkarasu (Department of Pathology and Laboratory Medicine, All India Institute of Medical Sciences) ;
  • Sudeep Khera (Department of Pathology and Laboratory Medicine, All India Institute of Medical Sciences) ;
  • Selvakumar B (Department of Surgical Gastroenterology, All India Institute of Medical Sciences) ;
  • Taruna Yadav (Department of Diagnostic and Interventional Radiology, All India Institute of Medical Sciences)
  • Received : 2023.03.30
  • Accepted : 2023.09.18
  • Published : 2023.11.30
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Abstract

Vascular tumors of the liver are mesenchymal lesions from endothelial cells. They range from common benign lesions such as haemangioma, intermediate tumors like Kaposi sarcoma, and perivascular epithelioid cell tumor to malignant tumors such as hepatic epithelioid hemangioendothelioma and hepatic angiosarcoma in adults. Pediatric vascular tumors of the liver also include benign, locally aggressive, borderline, and malignant masses with haemangiomas being the most common benign tumors and epithelioid hemangioendothelioma being an uncommon pediatric malignancy. The list of these lesions is completed by nodular regenerative hyperplasia, solitary fibrous tumour, and hepatic small vessel neoplasms (HSVN). Some of these tumors are uncommon and rare. This review article aimed to enumerate hepatic vascular tumors along with their imaging, histopathology, molecular findings for accurate diagnosis that can result in better management.

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References

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