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Radiologic Manifestations of Pulmonary Nuclear Protein in Testis Midline Carcinoma: A Case Report

폐에 발생한 고환 핵단백질 정중선 암의 영상의학적 소견: 증례 보고

  • Jung A Kim (Department of Radiology, Sanggye Paik Hospital, Inje University College of Medicine) ;
  • Mi-jin Kang (Department of Radiology, Sanggye Paik Hospital, Inje University College of Medicine) ;
  • Jung Yeon Kim (Department of Pathology, Sanggye Paik Hospital, Inje University College of Medicine) ;
  • Ji-Young Kim (Department of Radiology, Sanggye Paik Hospital, Inje University College of Medicine) ;
  • Soung Hee Kim (Department of Radiology, Sanggye Paik Hospital, Inje University College of Medicine) ;
  • Myeong Ja Jeong (Department of Radiology, Sanggye Paik Hospital, Inje University College of Medicine) ;
  • Ji Hae Lee (Department of Radiology, Sanggye Paik Hospital, Inje University College of Medicine)
  • 김정아 (인제대학교 의과대학 상계백병원 영상의학과) ;
  • 강미진 (인제대학교 의과대학 상계백병원 영상의학과) ;
  • 김정연 (인제대학교 의과대학 상계백병원 병리과) ;
  • 김지영 (인제대학교 의과대학 상계백병원 영상의학과) ;
  • 김성희 (인제대학교 의과대학 상계백병원 영상의학과) ;
  • 정명자 (인제대학교 의과대학 상계백병원 영상의학과) ;
  • 이지혜 (인제대학교 의과대학 상계백병원 영상의학과)
  • Received : 2022.04.18
  • Accepted : 2022.07.02
  • Published : 2023.03.01

Abstract

Nuclear portein in testis (NUT) midline carcinoma is a very rare and low-differentiating malignant epithelial tumor that differentiates very aggressively and has poor prognosis. NUT midline carcinoma occurring in the lungs in particular can be confused with other cancers because few cases have been reported in Korea to date and can show various histological forms. Reports of radiology findings are very rare worldwide. Here we report the imaging findings of pulmonary NUT midline carcinoma in a 25-year-old female along with pathological findings.

고환 핵단백질 정중선 암은 매우 드물고 분화가 나쁜, 악성 편평세포암의 한 하위 종양으로서 공격적으로 분화하여 예후가 좋지 않다. 특히 폐에서 발생하는 고환 핵단백질 정중선 암은 현재까지 국내에 보고된 증례가 많지 않고 다양한 조직학적 형태를 보일 수 있어 다른 암과 혼동될 수 있다. 영상의학적 소견의 보고는 전 세계적으로 매우 드문 편이다. 저자들은 25세 여성에서 발생한 폐 고환 핵단백질 정중선 암의 영상의학적 소견을 병리학적인 소견과 함께 보고하고자 한다.

Keywords

References

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