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Extrapleural Malignant Solitary Fibrous Tumor Presenting as Invasive Bilateral Paravertebral Tumors: A Case Report

침습성 양측 척추주위 종양으로 나타난 흉막외 악성 고립섬유 종양: 증례 보고

  • Jewon Jeong (Department of Radiology, Soonchunhyang University Seoul Hospital) ;
  • So-Young Jin (Department of Pathology, Soonchunhyang University Seoul Hospital)
  • 정제원 (순천향대학교 서울병원 영상의학과) ;
  • 진소영 (순천향대학교 서울병원 병리과)
  • Received : 2022.05.11
  • Accepted : 2022.06.18
  • Published : 2023.01.01

Abstract

Solitary fibrous tumors (SFTs) commonly arise from the pleura and are mostly benign. However, they may develop anywhere in the body, and 10%-30% are malignant. Classically, SFTs appear as solitary enhancing masses, and bilateral presentation is extremely rare. In this case, an 88-year-old male presented with back pain and a history of chronic tuberculous empyema. Imaging studies revealed bilateral paravertebral masses with aggressive radiologic features, which were speculatively presumed as thoracic malignancies in association with chronic empyema. Herein, we report a unique case of bilateral paravertebral malignant SFTs that were accurately diagnosed with a CT-guided coaxial needle biopsy.

고립성 섬유종은 흉막에서 흔히 발생하는 양성 종양으로 알려져 있으나, 신체 어느 곳에서나 발생할 수 있고 10%-30%에서는 악성이다. 전형적으로, 고립성 섬유종은 단일성의 조영증강되는 종괴로 나타나지만, 척추 주위의 양측성 종괴로 나타나는 경우는 보고되어 있지 않다. 이 증례에서는, 등 통증과 만성 농흉의 병력이 있던 88세 남자 환자의 영상 검사에서 침습적인 양측성 척추 주위 종괴가 발견되었고, 만성 농흉과 연관된 흉부 악성 종양을 먼저 의심하였다. CT 유도하 이중구조 바늘 생검을 통해 진단된 양측성의 척추 주위 악성 고립성 섬유종의 증례를 보고한다.

Keywords

References

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