Korean Journal of Head & Neck Oncology (대한두경부종양학회지)

The Korean Society for Head and Neck Oncology (대한두경부종양학회)
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A Case of Hemangioma of Nasal Cavity in Von Hippel-Lindau Syndrome

Von Hippel-Lindau 증후군 환자에서 발생한 비강내 혈관종

  • Hyun Seok Kang (Department of Otorhinolaryngology-Head and Neck Surgery, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Soo Jin Jung (Department of Otorhinolaryngology-Head and Neck Surgery, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Seoung Wan Chae (Department of Pathology, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine) ;
  • Seok Jin Hong (Department of Otorhinolaryngology-Head and Neck Surgery, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine)
  • 강현석 (성균관대학교 의과대학 강북삼성병원 이비인후과학교실) ;
  • 정수진 (성균관대학교 의과대학 강북삼성병원 이비인후과학교실) ;
  • 채승완 (성균관대학교 의과대학 강북삼성병원 병리학교실) ;
  • 홍석진 (성균관대학교 의과대학 강북삼성병원 이비인후과학교실)
  • Received : 2023.10.18
  • Accepted : 2023.11.11
  • Published : 2023.11.30
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Abstract

We report a unique case of hemangioma of the nasal cavity in von Hippel-Lindau (VHL) syndrome. A 26-year-old female with VHL syndrome who had previously undergone surgery for pancreatic and adrenal mass presented with a 4-month history of left-sided nasal obstruction. The patient had an expansile mass lesion in the left nasal cavity and an imaging test demonstrated the mass in the left maxillary sinus extending to the nasal cavity. The tumor was removed with an endoscopic prelacrimal recess approach considering the possibility of not only a benign tumor such as hemangioma but also a malignant tumor of the maxillary sinus and histopathologic examination confirmed cavernous hemangioma. This case is the rarely reported manifestation of the paranasal sinus in VHL disease.

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References

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