Annals of Hepato-Biliary-Pancreatic Surgery (한국간담췌외과학회지)

The Korean Association of Hepato-Biliary-Pancreatic Surgery (한국간담췌외과학회)
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Portal cavernoma cholangiopathy: Update and recommendations on diagnosis and management

  • Ruchir Bhavsar (Department of Surgical Gastroenterology and Liver Transplantation, Sir Ganga Ram Hospital) ;
  • Amitabh Yadav (Department of Surgical Gastroenterology and Liver Transplantation, Sir Ganga Ram Hospital) ;
  • Samiran Nundy (Department of Surgical Gastroenterology and Liver Transplantation, Sir Ganga Ram Hospital)
  • Received : 2022.05.17
  • Accepted : 2022.06.07
  • Published : 2022.11.30
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Abstract

Portal cavernoma cholangiopathy is defined as an obstruction of the biliary system due to distended veins surrounding bile ducts that mainly occur in patients with extrahepatic portal venous obstruction. The periductal venous plexuses encircling the ducts can cause morphological changes which may or may not become symptomatic. Currently, non-invasive techniques such as ultrasonography, computed tomography, magnetic resonance cholangiopancreatography, and dynamic contrast enhanced magnetic resonance images are being used to diagnose this disorder. Only a few patients who have symptoms of biliary obstruction require drainage which might be accomplished using endoscopic stenting, decompression of the portal venous system usually via a lienorenal shunt, a difficult direct hepaticojejunostomy, and rarely a liver transplant.

Keywords

Acknowledgement

Authors would like to acknowledge Dr. Kanika Dhawan for his perennial support in obtaining and maintaining patient records.

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