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CT Findings of Mucinous Adenocarcinoma Arising from the Renal Calyx in Horseshoe Kidney: A Case Report

말굽 신장의 신배에서 발생한 원발성 점액성 선암의 CT 소견: 증례 보고

  • Soul Han (Department of Radiology, Wonkwang University Hospital) ;
  • Young Hwan Lee (Department of Radiology, Wonkwang University Hospital) ;
  • Youe Ree Kim (Department of Radiology, Wonkwang University Hospital)
  • 한솔 (원광대학교병원 영상의학과) ;
  • 이영환 (원광대학교병원 영상의학과) ;
  • 김유리 (원광대학교병원 영상의학과)
  • Received : 2022.03.21
  • Accepted : 2022.07.20
  • Published : 2022.11.01

Abstract

Mucinous adenocarcinoma of the kidney is an extremely rare cystic malignant tumor with a poor prognosis that occurs in the pelvicalyceal system. Pre-opeartive diagnosis is very difficult because the tumor's clinical and imaging features are nonspecific. Here we report a case of primary mucinous adenocarcinoma arising from the horseshoe kidney in a 69-year-old male, focusing on CT findings. The tumor was a complex cystic mass with irregular wall thickening, multifocal calcifications, and septa and progressed to pseudomyxoma peritonei postoperatively.

신장의 점액성 선암은 신우신배계에서 발생하는 매우 드문 낭성 악성 종양으로 예후가 좋지 않다. 임상 증상 및 영상학적 소견이 비특이적이어서 수술 전 진단이 매우 어렵다. 저자들은 69세 남자 환자의 말굽신장에서 발생한 원발성 점액성 선암의 증례를 CT 소견을 중심으로 보고한다. 이 종양은 불규칙한 벽비후와 다수의 석회화 및 중격을 동반한 복합 낭종으로 관찰되었고 수술 후 복막강거짓점액종으로 진행하였다.

Keywords

References

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