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대혈관 혈관염이 첫 번째 징후로 나타난 급성 골수성 백혈병: 증례 보고

Large Vessel Vasculitis as an Initial Manifestation of Acute Myeloid Leukemia: A Case Report

  • 전가영 (대구파티마병원 영상의학과) ;
  • 양동진 (대구파티마병원 영상의학과) ;
  • 장종창 (대구파티마병원 영상의학과) ;
  • 강종완 (대구파티마병원 내과)
  • Gayoung Jeon (Department of Radiology, Daegu Fatima Hospital) ;
  • Dongjin Yang (Department of Radiology, Daegu Fatima Hospital) ;
  • Jongchang Jang (Department of Radiology, Daegu Fatima Hospital) ;
  • Jongwan Kang (Department of Internal Medicine, Daegu Fatima Hospital)
  • 투고 : 2021.06.16
  • 심사 : 2021.09.23
  • 발행 : 2022.07.01

초록

대혈관 혈관염은 대동맥과 이것의 주요 분지의 혈관벽에 만성 염증이 생기는 질환으로써 면역 이상반응에 의한 것이다. 혈액암은 이차적인 혈관염의 아주 드문 원인 중 한 가지다. 우리는 일차성 혈관염을 모방한 급성 골수성 백혈병과 연관된 드문 형태의 대혈관 혈관염에 대해서 보고하고자 한다.

Large vessel vasculitis is characterized by chronic inflammation within the aortic wall and its major branches. The inflammation is considered to occur as a result of immune dysregulation. Hematologic malignancy is one of the rare causes of secondary vasculitis. Herein, we report a rare case of large vessel vasculitis associated with acute myeloid leukemia mimicking primary vasculitis.

키워드

참고문헌

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