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CT and MRI Features of Middle Ear Fibrous Hamartoma of Infancy: A Case Report

중이에서 발견된 영유아 섬유성 과오종의 영상 소견: 증례 보고

  • Sang Hun Baek (Department of Radiology, Dong-A University Medical Center, Dong-A University College of Medicine) ;
  • Sanghyeon Kim (Department of Radiology, Dong-A University Medical Center, Dong-A University College of Medicine) ;
  • Kyungjae Lim (Department of Radiology, Dong-A University Medical Center, Dong-A University College of Medicine)
  • 백상훈 (동아대학교 의과대학 동아대학교의료원 영상의학과) ;
  • 김상현 (동아대학교 의과대학 동아대학교의료원 영상의학과) ;
  • 임경재 (동아대학교 의과대학 동아대학교의료원 영상의학과)
  • Received : 2021.04.21
  • Accepted : 2021.06.23
  • Published : 2022.03.01

Abstract

Fibrous hamartoma of infancy in the middle ear is extremely rare. We report the case of a 26-month-old male patient who presented with a mass in the left middle ear. A temporal bone CT scan showed complete opacification of the left middle ear and mastoid air cells without ossicular erosion. On MRI, the mass revealed heterogeneous signal intensities indicative of fat and fibrous components. A definitive diagnosis was made postoperatively based on the histological results. Although rare, fibrous hamartoma of infancy should be considered as a differential diagnosis of a middle ear mass during childhood.

중이의 영유아 섬유성 과오종은 매우 드물다. 저자들은 26개월 남아의 중이에서 진단된 사례를 영상의학적 소견을 중심으로 보고하고자 한다. CT 영상에서는 귓속뼈의 파괴가 없었으며 MRI에서는 지방과 섬유성 조직과 유사한 신호 강도를 보였다. 수술 후 조직학적 검사에서 영유아 섬유성 과오종으로 진단받았다. 중이의 영유아 섬유성 과오종은 드물지만, 유년기에 중이에서 관찰되는 종괴의 감별진단에 포함되어야 한다.

Keywords

References

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