대한영상의학회지 (Journal of the Korean Society of Radiology)

  • 제83권3호
  • /
  • Pages.730-736
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  • 2022
  • /
  • 1738-2637(pISSN)
  • /
  • 2288-2928(eISSN)
대한영상의학회 (The Korean Society of Radiology)
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천공으로 발현된 소아 환자에서의 장 신경절신경종증: 증례 보고와 문헌 고찰

Intestinal Ganglioneuromatosis in a Pediatric Patient Presenting as Perforation: A Case Report and Literature Review

  • 이님 (이화여자대학교 의과대학 이화여자대학교 목동병원 영상의학과) ;
  • 조현혜 (이화여자대학교 의과대학 이화여자대학교 목동병원 영상의학과) ;
  • 조민선 (이화여자대학교 의과대학 이화여자대학교 서울병원 병리학과)
  • Nim Lee (Departments of Radiology, Medical Research Institute, College of Medicine, Ewha Womans University Mokdong Hospital) ;
  • Hyun-Hae Cho (Departments of Radiology, Medical Research Institute, College of Medicine, Ewha Womans University Mokdong Hospital) ;
  • Min-Sun Cho (Departments of Pathology, Medical Research Institute, College of Medicine, Ewha Womans University Seoul Hospital)
  • 투고 : 2021.03.27
  • 심사 : 2021.07.17
  • 발행 : 2022.05.01
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초록

장 신경절신경종증은 특히 소아 환자에서 매우 드물며 특히 질병의 영상의학적 소견에 대한 보고가 부족하다. 이에 저자들은 이 질환의 드문 초기 증상인 장 천공을 동반한 횡행 및 비장굴곡의 결장을 포함하는 장 신경절신경종증의 소아 사례를 제시한다.

Intestinal ganglioneuromatosis is an extremely rare condition, particularly in pediatric patients, and the imaging features of the disease have been rarely reported before. Herein, we present a pediatric case of intestinal ganglioneuromatosis involving the transverse colon and splenic flexure with bowel perforation, which is a rare initial manifestation of the disease.

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참고문헌

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