Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Intestinal Ganglioneuromatosis in a Pediatric Patient Presenting as Perforation: A Case Report and Literature Review

천공으로 발현된 소아 환자에서의 장 신경절신경종증: 증례 보고와 문헌 고찰

  • Nim Lee (Departments of Radiology, Medical Research Institute, College of Medicine, Ewha Womans University Mokdong Hospital) ;
  • Hyun-Hae Cho (Departments of Radiology, Medical Research Institute, College of Medicine, Ewha Womans University Mokdong Hospital) ;
  • Min-Sun Cho (Departments of Pathology, Medical Research Institute, College of Medicine, Ewha Womans University Seoul Hospital)
  • 이님 (이화여자대학교 의과대학 이화여자대학교 목동병원 영상의학과) ;
  • 조현혜 (이화여자대학교 의과대학 이화여자대학교 목동병원 영상의학과) ;
  • 조민선 (이화여자대학교 의과대학 이화여자대학교 서울병원 병리학과)
  • Received : 2021.03.27
  • Accepted : 2021.07.17
  • Published : 2022.05.01
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Abstract

Intestinal ganglioneuromatosis is an extremely rare condition, particularly in pediatric patients, and the imaging features of the disease have been rarely reported before. Herein, we present a pediatric case of intestinal ganglioneuromatosis involving the transverse colon and splenic flexure with bowel perforation, which is a rare initial manifestation of the disease.

장 신경절신경종증은 특히 소아 환자에서 매우 드물며 특히 질병의 영상의학적 소견에 대한 보고가 부족하다. 이에 저자들은 이 질환의 드문 초기 증상인 장 천공을 동반한 횡행 및 비장굴곡의 결장을 포함하는 장 신경절신경종증의 소아 사례를 제시한다.

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References

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