Journal of Yeungnam Medical Science

Yeungnam University College of Medicine, Yeungnam University Institute Medical Science (영남대 의대 학술지 편집위원회)
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Enteritis cystica profunda with lipoma in the second portion of the duodenum: a case report

  • Shim, Beom Jin (Division of Gastroenterology, Department of Internal Medicine, Maryknoll Medical Center) ;
  • Park, Seung Keun (Division of Gastroenterology, Department of Internal Medicine, Maryknoll Medical Center) ;
  • Park, Hee Ug (Division of Gastroenterology, Department of Internal Medicine, Maryknoll Medical Center) ;
  • Park, Tae Young (Division of Gastroenterology, Department of Internal Medicine, Maryknoll Medical Center)
  • Received : 2021.04.23
  • Accepted : 2021.05.14
  • Published : 2022.01.31
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Abstract

Enteritis cystica profunda (ECP), a rare and benign condition, is defined as the displacement of the glandular epithelium into the submucosa and more profound layers of the small intestinal wall leading to the formation of mucin-filled cystic spaces. ECP frequently occurs in the ileum or jejunum and is associated with diseases such as Crohn disease and Peutz-Jeghers syndrome. ECP also develops in the absence of known pathology. ECP in the duodenum is very rare and mostly occurs without associated conditions. In this report, we present a rare case of ECP without an associated disease, in the second portion of the duodenum distal to the ampulla of Vater and coexisting with lipoma within the polypoid lesion.

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References

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