Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Transcatheter Arterial Embolization of a Ruptured Superior Rectal Artery Aneurysm in Type 1 Neurofibromatosis: A Case Report

신경섬유종증 1형에서 발생한 파열된 상직장동맥류의 경도관 동맥 색전술: 증례 보고

  • Se Jin Park (Department of Radiology, Daegu Catholic University College of Medicine) ;
  • Young Hwan Kim (Department of Radiology, Daegu Catholic University College of Medicine) ;
  • Ung Rae Kang (Department of Radiology, Daegu Catholic University College of Medicine) ;
  • Seung Woo Ji (Department of Radiology, CHA Gumi Medical Center, CHA University)
  • 박세진 (대구가톨릭대학교 의과대학 영상의학과) ;
  • 김영환 (대구가톨릭대학교 의과대학 영상의학과) ;
  • 강웅래 (대구가톨릭대학교 의과대학 영상의학과) ;
  • 지승우 (차의과학대학교 부속 구미차병원 영상의학과)
  • Received : 2019.06.05
  • Accepted : 2019.08.15
  • Published : 2020.05.01
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Abstract

Neurofibromatosis type 1 (NF1) is a common autosomal-dominant disorder. Vasculopathies associated with NF1 are rare and can cause aneurysms, stenoses, and arteriovenous malformations. Aneurysms may rupture spontaneously, which could be fatal. Spontaneous mesenteric hemorrhage due to rupture of an inferior mesenteric artery aneurysm associated with NF1 has rarely been reported. Herein, we report a case of spontaneous rupture of a fusiform aneurysm in the superior rectal artery in a 56-year-old woman with NF1 who was successfully treated with transcatheter arterial embolization.

신경섬유종증 1형은 상염색체우성질환으로 가장 흔한 유전 질환 중 하나이다. 혈관병증은 드물게 발생할 수 있으며, 신경섬유종증 1형 혈관병증은 동맥류, 협착, 동정맥기형의 형태로 나타난다. 동맥류의 경우 자연파열과 같은 치명적인 합병증을 유발할 수 있다. 신경섬유종증 1형과 연관된 하장간막동맥류의 파열로 인한 장간막출혈은 매우 드물게 보고되고 있다. 이에 저자들은 신경섬유종증 1형에 의한 방추형 상직장동맥류의 자발적 파열로 내원한 56세 여성환자에서 코일을 이용한 경도관 동맥 색전술을 시행하여 성공적으로 치료한 1예를 경험하였기에 이를 보고하고자 한다.

Keywords

References

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