Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Aortic Valve-Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult

  • Shin, Hong Ju (Department of Thoracic and Cardiovascular Surgery, Korea University Ansan Hospital, Korea University College of Medicine) ;
  • Shin, Jae Seung (Department of Thoracic and Cardiovascular Surgery, Korea University Ansan Hospital, Korea University College of Medicine)
  • Received : 2019.04.03
  • Accepted : 2020.02.09
  • Published : 2020.06.05
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Abstract

Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.

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References

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