Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Cardiac Autotransplantation with Concurrent Pneumonectomy for Complete Resection of Primary Cardiac Intimal Sarcoma

  • Ku, Min Jung (Department of Thoracic and Cardiovascular Surgery, Jeju National University Hospital) ;
  • Kim, Su Wan (Department of Thoracic and Cardiovascular Surgery, Jeju National University Hospital) ;
  • Lee, Seogjae (Department of Thoracic and Cardiovascular Surgery, Jeju National University Hospital) ;
  • Chang, Jee Won (Department of Thoracic and Cardiovascular Surgery, Jeju National University Hospital) ;
  • Lee, Jonggeun (Department of Thoracic and Cardiovascular Surgery, Jeju National University Hospital) ;
  • Jeong, Dong Seop (Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • Received : 2019.07.23
  • Accepted : 2019.10.30
  • Published : 2020.06.05
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Abstract

Primary cardiac sarcoma is rare, and intimal sarcoma is an extremely rare and highly lethal disease. We report a case of a 62-year-old woman who was incidentally diagnosed with a primary cardiac sarcoma originating from the left atrial appendage and extending to the left superior pulmonary vein. The location of the tumor was very complicated, posing a major challenge for complete resection. We successfully performed complete resection of the cardiac sarcoma via cardiac autotransplantation with left pneumonectomy. The patient recovered uneventfully, without any adjuvant therapy as of 6 months postoperatively. Autotransplantation of the heart may be suggested as a reasonable surgical option for extensive left atrial tumors.

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References

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