Investigative Magnetic Resonance Imaging

Korean Society of Magnetic Resonance in Medicine (대한자기공명의과학회)
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A Case of Idiopathic Infratentorial Superficial Siderosis

  • Shin, Daeun (Department of Neurology, Kyungpook National University Hospital) ;
  • Yang, Seok-Yul (Department of Neurology, Kyungpook National University Hospital) ;
  • Kim, Youngwook (Department of Neurology, Kyungpook National University Hospital) ;
  • Ryu, Ho-Sung (Department of Neurology, Kyungpook National University Hospital) ;
  • Lee, Hoseok (Department of Radiology, Kyungpook National University Hospital)
  • Received : 2019.09.18
  • Accepted : 2019.11.11
  • Published : 2020.03.30
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Abstract

Superficial siderosis is attributed to hemosiderin deposition in the subpial layers of the nervous system. The clinical features of infratentorial superficial siderosis (ISS) are hearing loss, cerebellar ataxia, and corticospinal tract signs and the most common cause of idiopathic ISS is a dural defect. As magnetic resonance imaging (MRI) has advanced, the diagnosis of infratentorial superficial siderosis can be confirmed by unique radiological findings in MRI. Here, we report on a female patient diagnosed with idiopathic ISS by means of clinical symptoms and radiological findings.

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References

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