Journal of the Korean neurological association (대한신경과학회지)

Korean Neurological Association (대한신경과학회)
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Ischemic Stroke with Cerebral Vasculopathy in POEMS Syndrome

POEMS 증후군 환자의 뇌혈관병증에 의한 뇌졸중

  • Kang, Sung Woo (Department of Neurology, Severance Hospital, Yonsei University of College of Medicine) ;
  • Choi, Bo Kyu (Department of Neurology, Severance Hospital, Yonsei University of College of Medicine) ;
  • Han, Hee Jo (Department of Neurology, Severance Hospital, Yonsei University of College of Medicine) ;
  • Cho, Soo Mi (Department of Neurology, Severance Hospital, Yonsei University of College of Medicine) ;
  • Cha, Jihoon (Department of Radiology, Severance Hospital, Yonsei University of College of Medicine) ;
  • Nam, Hyo Suk (Department of Neurology, Severance Hospital, Yonsei University of College of Medicine) ;
  • Heo, Ji Hoe (Department of Neurology, Severance Hospital, Yonsei University of College of Medicine) ;
  • Kim, Young Dae (Department of Neurology, Severance Hospital, Yonsei University of College of Medicine)
  • 강성우 (연세대학교 의과대학 세브란스병원 신경과) ;
  • 최보규 (연세대학교 의과대학 세브란스병원 신경과) ;
  • 한희조 (연세대학교 의과대학 세브란스병원 신경과) ;
  • 조수미 (연세대학교 의과대학 세브란스병원 신경과) ;
  • 차지훈 (연세대학교 의과대학 세브란스병원 영상의학과) ;
  • 남효석 (연세대학교 의과대학 세브란스병원 신경과) ;
  • 허지회 (연세대학교 의과대학 세브란스병원 신경과) ;
  • 김영대 (연세대학교 의과대학 세브란스병원 신경과)
  • Received : 2018.07.20
  • Accepted : 2018.09.27
  • Published : 2018.11.30
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Abstract

Ischemic stroke caused by the cerebral vasculopathy is a rare complication of polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome. We present a case of recurrent ischemic strokes caused by cerebral vasculopathy in a patient with POEMS syndrome. A 34-year-old man presented with gait disturbance and dizziness. Brain magnetic resonance imaging demonstrated acute ischemic stroke in the middle cerebral artery-anterior cerebral artery (MCA-ACA) border zones of bilateral hemispheres. Repeated angiographic studies showed progressive worsening of the left distal internal carotid artery, ACA, and MCA stenoses, along with sustained steno-occlusion of right MCA.

Keywords

References

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