Journal of Electrodiagnosis and Neuromuscular Diseases (대한근전도전기진단의학회지)

Korean Association of EMG Electrodiagnostic Medicine (대한근전도전기진단의학회)
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Severe Paraspinal Muscle Atrophy with Fatty Degeneration in a Young Adult: A Case Report

젊은 성인의 척추주위근에 발생한 지방 변성을 동반한 심한 근위축: 증례보고

  • Huh, Jae-Won (Department of Rehabilitation Medicine, School of Medicine, Kyungpook National University) ;
  • Yang, Won-Jong (Department of Rehabilitation Medicine, School of Medicine, Kyungpook National University) ;
  • Park, Eunhee (Department of Rehabilitation Medicine, School of Medicine, Kyungpook National University) ;
  • Lee, Jae Eun (Department of Rehabilitation Medicine, School of Medicine, Kyungpook National University) ;
  • Kim, Chul-Hyun (Department of Rehabilitation Medicine, School of Medicine, Kyungpook National University)
  • 허재원 (경북대학교 의과대학 재활의학교실) ;
  • 양원종 (경북대학교 의과대학 재활의학교실) ;
  • 박은희 (경북대학교 의과대학 재활의학교실) ;
  • 이재은 (경북대학교 의과대학 재활의학교실) ;
  • 김철현 (경북대학교 의과대학 재활의학교실)
  • Received : 2018.05.18
  • Accepted : 2018.07.16
  • Published : 2018.12.31
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Abstract

A 36-year-old male patient developed diffuse low back pain. His past medical history was unremarkable and had no family history of neuromuscular disease. He had no bladder and bowel problems. Creatine kinase was 172 U/L (normal < 170). Other fluid and blood chemistry tests were normal. Manual muscle test grades of extremities and sensory examination were normal. Muscle stretch reflexes were normal. Fasciculations and myotonia were not detected. Straight leg raising test was negative. There was no spinal root compression, spinal stenosis, or signal intensity change of spinal cord on magnetic resonance imaging (MRI). Fatty change and atrophy of the cervical, thoracic and lumbar paraspinal muscles were noted on MRI. Nerve conduction studies were normal. Electromyography showed 1+ positive sharp waves in the lumbar paraspinal muscles. Electromyography of upper and lower extremity muscles revealed no abnormal spontaneous activity. We report a rare case of severe paraspinal muscle atrophy with fatty degeneration in a Young Adult.

Keywords

References

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