The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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Ileocecal Mucosal Involvement of Blastic Plasmacytoid Dendritic Cell Neoplasm without Skin Lesions

대장 점막을 침범한 피부 병변이 없는 Blastic Plasmacytoid Dendritic Cell Neoplasm 1예

  • Choi, Hyun Ju (Division of Gastroenterology, Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Park, Jongha (Division of Gastroenterology, Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Lee, Jin (Division of Gastroenterology, Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Kim, Mi Young (Division of Gastroenterology, Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Jeong, Heui Jeong (Division of Gastroenterology, Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Lee, Ji Woon (Division of Gastroenterology, Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Kim, Bomi (Department of Pathology, Haeundae Paik Hospital, Inje University College of Medicine)
  • 최현주 (인제대학교 의과대학 해운대백병원 소화기내과) ;
  • 박종하 (인제대학교 의과대학 해운대백병원 소화기내과) ;
  • 이진 (인제대학교 의과대학 해운대백병원 소화기내과) ;
  • 김미령 (인제대학교 의과대학 해운대백병원 소화기내과) ;
  • 정희정 (인제대학교 의과대학 해운대백병원 소화기내과) ;
  • 이지운 (인제대학교 의과대학 해운대백병원 소화기내과) ;
  • 김보미 (인제대학교 의과대학 해운대백병원 병리과)
  • Received : 2017.11.08
  • Accepted : 2018.02.18
  • Published : 2018.10.01
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Abstract

Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a relatively rare hematological malignancy, and most cases present with characteristic skin lesions. The skin lesions appear as nodules, plaques, and bruise-like macules with redness or ulcerations. BPDCN without skin lesions is rare. Cases with hepatosplenomegaly, pulmonary involvement, multiple lymphadenopathies, renal masses, sinonasal sinus, and subcutaneous masses have also been reported. Here, we report the first case of ileocecal valve involvement of BPDCN without skin lesions.

BPDCN은 드문 혈액종양으로 80%에서 피부 병변을 동반한다. 피부 병변을 동반하지 않는 BPDCN은 이전 문헌 고찰에 따르면 폐침범, 연부 조직 종괴 등으로 내원하여 경피적 조직 검사로 진단된 경우가 대부분이다. 저자들은 피부 병변을 동반하지 않은 BPDCN을 대장 내시경을 통한 조직 검사와 해당 임파선의 조직 검사를 통하여 진단한 증례를 보고한다.

Keywords

References

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