Vascular Specialist International

The Korean Society for Vascular Surgery (대한혈관외과학회)
권호 표지
DOI QR코드

DOI QR Code

Hybrid Approach of Ruptured Type B Aortic Dissection with an Aberrant Subclavian Artery in a Single Patient with Turner Syndrome: A Case Report

  • Son, Shin-Ah (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Kyungpook National University, Kyungpook National University Hospital) ;
  • Lim, Kyoung Hoon (Department of Surgery, Trauma Center, School of Medicine, Kyungpook National University, Kyungpook National University Hospital) ;
  • Kim, Gun-Jik (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Kyungpook National University, Kyungpook National University Hospital)
  • Received : 2018.09.01
  • Accepted : 2018.11.14
  • Published : 2018.12.31
⟨ Previous Next ⟩

Abstract

Turner syndrome, also described as 45, X, may present with most serious cardiovascular anomalies including risk of aortic dissection and rupture. In emergency situation, management for aortic dissection with complicated anatomy accompanying vascular anomaly is challenging. Here, we report a rare case of ruptured type B aortic dissection with aberrant subclavian artery and partial anomalous pulmonary venous connection in a Turner syndrome. Through right carotid-subclavian artery bypass and thoracic endovascular aortic repair, successful hybrid endovascular management correlated with a favorable result in this emergency situation.

Keywords

References

  1. Sybert VP. Cardiovascular malformations and complications in Turner syndrome. Pediatrics 1998;101:E11.
  2. Bondy CA. Congenital cardiovascular disease in Turner syndrome. Congenit Heart Dis 2008;3:2-15. https://doi.org/10.1111/j.1747-0803.2007.00163.x
  3. Gravholt CH, Landin-Wilhelmsen K, Stochholm K, Hjerrild BE, Ledet T, Djurhuus CB, et al. Clinical and epidemiological description of aortic dissection in Turner's syndrome. Cardiol Young 2006;16:430-436. https://doi.org/10.1017/S1047951106000928
  4. Ho VB, Bakalov VK, Cooley M, Van PL, Hood MN, Burklow TR, et al. Major vascular anomalies in Turner syndrome: prevalence and magnetic resonance angiographic features. Circulation 2004;110:1694-1700. https://doi.org/10.1161/01.CIR.0000142290.35842.B0
  5. Stochholm K, Juul S, Juel K, Naeraa RW, Gravholt CH. Prevalence, incidence, diagnostic delay, and mortality in Turner syndrome. J Clin Endocrinol Metab 2006;91:3897-3902. https://doi.org/10.1210/jc.2006-0558
  6. Bondy CA. Aortic dissection in Turner syndrome. Curr Opin Cardiol 2008;23:519-526. https://doi.org/10.1097/HCO.0b013e3283129b89
  7. Dawson-Falk KL, Wright AM, Bakker B, Pitlick PT, Wilson DM, Rosenfeld RG. Cardiovascular evaluation in Turner syndrome: utility of MR imaging. Australas Radiol 1992;36:204-209. https://doi.org/10.1111/j.1440-1673.1992.tb03152.x
  8. Moore JW, Kirby WC, Rogers WM, Poth MA. Partial anomalous pulmonary venous drainage associated with 45,X Turner's syndrome. Pediatrics 1990;86:273-276.
  9. Snellen HA, van Ingen HC, Hoefsmit EC. Patterns of anomalous pulmonary venous drainage. Circulation 1968;38:45-63. https://doi.org/10.1161/01.CIR.38.1.45
  10. Harrison LH Jr, Batson RC, Hunter DR. Aberrant right subclavian artery aneurysm: an analysis of surgical options. Ann Thorac Surg 1994;57:1012-1014. https://doi.org/10.1016/0003-4975(94)90225-9
  11. Carlson M, Silberbach M. Dissection of the aorta in Turner syndrome: two cases and review of 85 cases in the literature. J Med Genet 2007;44:745-749. https://doi.org/10.1136/jmg.2007.052019
  12. Klein LW, Levin JL, Weintraub WS, Agarwal JB, Helfant RH. Pseudocoarctation of the aortic arch in a patient with Turner's syndrome. Clin Cardiol 1984;7:621-623. https://doi.org/10.1002/clc.4960071114
  13. Burgess BJ, Iftikhar K. Aortic dissection in a case of Turner's syndrome. Emerg Med J 2009;26:908. https://doi.org/10.1136/emj.2008.068122
  14. Matura LA, Ho VB, Rosing DR, Bondy CA. Aortic dilatation and dissection in Turner syndrome. Circulation 2007; 116:1663-1670. https://doi.org/10.1161/CIRCULATIONAHA.106.685487
  15. Cooper DG, Markur S, Walsh SR, Cousins C, Hayes PD, Boyle JR. Hybrid endovascular repair of an aneurysmal chronic type B dissection in a patient with Marfan syndrome with an aberrant right subclavian artery. Vasc Endovascular Surg 2009;43:271-276. https://doi.org/10.1177/1538574408328662

Cited by

  1. One-stage supraclavicular hybrid procedure for type B aortic dissection involving three rare anatomical anomalies: a case report and literature review vol.49, pp.6, 2018, https://doi.org/10.1177/03000605211020241