Korean Journal of Otorhinolaryngology-Head and Neck Surgery

Korean Society of Otolaryngology-Head and Neck Surgery (대한이비인후과학회)
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Congenital Cholesteatoma of Mastoid Temporal Bone and Posterior Cranial Fossa Treated with Transmastoid Marsupialization

유양동과 후두개와에 위치하는 선천성 진주종의 경유양동 조대술을 통한 치료

  • Sung, Chung Man (Department of Otolaryngology-Head and Neck Surgery, Chonnam National University Medical School and Chonnam National University Hospital) ;
  • Yang, Hyung Chae (Department of Otolaryngology-Head and Neck Surgery, Chonnam National University Medical School and Chonnam National University Hospital) ;
  • Cho, Yong Beom (Department of Otolaryngology-Head and Neck Surgery, Chonnam National University Medical School and Chonnam National University Hospital) ;
  • Jang, Chul Ho (Department of Otolaryngology-Head and Neck Surgery, Chonnam National University Medical School and Chonnam National University Hospital)
  • 성충만 (전남대학교 의과대학 전남대학교병원 이비인후과학교실) ;
  • 양형채 (전남대학교 의과대학 전남대학교병원 이비인후과학교실) ;
  • 조용범 (전남대학교 의과대학 전남대학교병원 이비인후과학교실) ;
  • 장철호 (전남대학교 의과대학 전남대학교병원 이비인후과학교실)
  • Received : 2017.04.05
  • Accepted : 2017.06.10
  • Published : 2018.12.25
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Abstract

A congenital cholesteatoma is a benign mass formed from the keratinizing stratified squamous epithelium. It usually occurs in young children's anterosuperior part of the middle ear. A congenital cholesteatoma which originates from mastoid temporal bone or expands to posterior cranial fossa is rare. Standard treatment of an intracranial cholesteatoma is surgical removal with craniotomy. A 69-year-old woman was diagnosed with a congenital cholesteatoma of mastoid temporal bone that expanded to the posterior cranial fossa, which was successfully treated with transmastoid marsupialization without craniotomy. This is a first documented case of a congenital cholesteatoma of mastoid temporal bone that expanded to posterior cranial fossa, which was successfully treated with transmastoid marsupialization without craniotomy.

Keywords

Acknowledgement

Supported by : National Research Foundation of Korea (NRF)

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