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Congenital Cholesteatoma of Mastoid Temporal Bone and Posterior Cranial Fossa Treated with Transmastoid Marsupialization

유양동과 후두개와에 위치하는 선천성 진주종의 경유양동 조대술을 통한 치료

  • Sung, Chung Man (Department of Otolaryngology-Head and Neck Surgery, Chonnam National University Medical School and Chonnam National University Hospital) ;
  • Yang, Hyung Chae (Department of Otolaryngology-Head and Neck Surgery, Chonnam National University Medical School and Chonnam National University Hospital) ;
  • Cho, Yong Beom (Department of Otolaryngology-Head and Neck Surgery, Chonnam National University Medical School and Chonnam National University Hospital) ;
  • Jang, Chul Ho (Department of Otolaryngology-Head and Neck Surgery, Chonnam National University Medical School and Chonnam National University Hospital)
  • 성충만 (전남대학교 의과대학 전남대학교병원 이비인후과학교실) ;
  • 양형채 (전남대학교 의과대학 전남대학교병원 이비인후과학교실) ;
  • 조용범 (전남대학교 의과대학 전남대학교병원 이비인후과학교실) ;
  • 장철호 (전남대학교 의과대학 전남대학교병원 이비인후과학교실)
  • Received : 2017.04.05
  • Accepted : 2017.06.10
  • Published : 2018.12.25

Abstract

A congenital cholesteatoma is a benign mass formed from the keratinizing stratified squamous epithelium. It usually occurs in young children's anterosuperior part of the middle ear. A congenital cholesteatoma which originates from mastoid temporal bone or expands to posterior cranial fossa is rare. Standard treatment of an intracranial cholesteatoma is surgical removal with craniotomy. A 69-year-old woman was diagnosed with a congenital cholesteatoma of mastoid temporal bone that expanded to the posterior cranial fossa, which was successfully treated with transmastoid marsupialization without craniotomy. This is a first documented case of a congenital cholesteatoma of mastoid temporal bone that expanded to posterior cranial fossa, which was successfully treated with transmastoid marsupialization without craniotomy.

Keywords

Acknowledgement

Supported by : National Research Foundation of Korea (NRF)

References

  1. Axon PR, Fergie N, Saeed SR, Temple RH, Ramsden RT. Petrosal cholesteatoma: management considerations for minimizing morbidity. Am J Otol 1999;20(4):505-10.
  2. Constans JP, Meder JF, De Divitiis E, Donzelli R, Maiuri F. Giant intradiploic epidermoid cysts of the skull. Report of two cases. J Neurosurg 1985;62(3):445-8. https://doi.org/10.3171/jns.1985.62.3.0445
  3. Lee DH. Intradiploic epidermoid cyst of the temporal bone: is it the same as or different from cholesteatoma? J Craniofac Surg 2011;22(5):1973-5. https://doi.org/10.1097/SCS.0b013e31822eaa52
  4. Clark MP, Pretorius PM, Beaumont D, Milford CA. Congenital cholesteatoma of occipital bone or intradiploic epidermoid cyst? One and the same disease. J Laryngol Otol 2009;123(6):673-5. https://doi.org/10.1017/S0022215108003083
  5. Warren FM, Bennett ML, Wiggins RH 3rd, Saltzman KL, Blevins KS, Shelton C, et al. Congenital cholesteatoma of the mastoid temporal bone. Laryngoscope 2007;117(8):1389-94. https://doi.org/10.1097/MLG.0b013e3180645d50
  6. Arana E, Latorre FF, Revert A, Menor F, Riesgo P, Liano F, et al. Intradiploic epidermoid cysts. Neuroradiology 1996;38(4):306-11. https://doi.org/10.1007/BF00596575
  7. Shellenberger DL, Roehm PC, Gantz B. Large extradural epidermoid tumor of the temporal bone and posterior fossa cranium. Otol Neurotol 2006;27(7):1043-4. https://doi.org/10.1097/01.mao.0000169052.46383.9d
  8. Jaiswal AK, Mahapatra AK. Giant intradiploic epidermoid cysts of the skull. A report of eight cases. Br J Neurosurg 2000;14(3):225-8. https://doi.org/10.1080/026886900408405
  9. Kim MJ, Chang KH, Han GC. Large intradiploic epidermoid cyst of the temporal bone. J Int Adv Otol 2014;10(2):187-9. https://doi.org/10.5152/iao.2014.30
  10. Sadato N, Numaguchi Y, Geisler FH, Kristt DA. Extradural epidermoid cyst occluding the transverse sinus: a case report. Comput Med Imaging Graph 1991;15(2):129-32. https://doi.org/10.1016/0895-6111(91)90038-W