Annals of Clinical Neurophysiology

The Korean Society of Clinical Neurophysiology (대한임상신경생리학회)
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Electrophysiological and radiological evidence for the multifocal nature of a case of multifocal acquired demyelinating sensory and motor neuropathy

  • Seong, Gi-Hun (Department of Neurology, Hallym University Sacred Heart Hospital) ;
  • Bae, Jong Seok (Department of Neurology, Kangdong Sacred Heart Hospital) ;
  • Ryu, Sanghyo (Department of Neurology, Haedong Hospital)
  • Received : 2018.06.18
  • Accepted : 2018.07.04
  • Published : 2018.07.31
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Abstract

Multifocal acquired demyelinating sensory and motor (MADSAM) neuropathy is a variant of chronic acquired demyelinating polyneuropathy. A 65-year-old women presented with upper arm weakness. A nerve conduction study showed conduction blocks over intermediate segments with sparing of distal compound action potentials. Magnetic resonance imaging revealed asymmetric hypertrophy of the brachial plexus on the affected side. These findings represent important electrophysiological and radiological evidence of MADSAM neuropathy. The condition of the patient began to improve after starting intravenous immunoglobulin administration.

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References

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