The Korean journal of internal medicine

  • 제33권5호
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  • Pages.841-850
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  • 2018
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  • 1226-3303(pISSN)
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  • 2005-6648(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
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DOI QR코드

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Immunoglobulin G4-related sclerosing cholangitis

  • Goodchild, George (Department of Gastroenterology, University College Hospital) ;
  • Pereira, Stephen P. (Department of Gastroenterology, University College Hospital) ;
  • Webster, George (Department of Gastroenterology, University College Hospital)
  • 투고 : 2018.01.09
  • 심사 : 2018.02.06
  • 발행 : 2018.09.01
⟨ 이전 논문 다음 논문 ⟩

초록

Immunoglobulin G4-related disease (IgG4-RD) is a systemic fibroinflammatory condition of which IgG4-related sclerosing cholangitis (IgG4-SC) is the biliary manifestation. In this review, we provide an overview of IgG4-RD, with a focus on the biliary manifestations. In particular, we describe the important differential diagnoses of IgG4-SC, namely, primary sclerosing cholangitis and cholangiocarcinoma, outline diagnostic criteria for IgG4-SC, provide insight into possible pathophysiological mechanisms underlying the disease and discuss short and long-term management options of this recently described disease.

키워드

과제정보

연구 과제 주관 기관 : National Institute for Health Research (NIHR)

참고문헌

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