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A case of nasopharyngeal mucoepidermoid carcinoma in a 5 year-old female patient

소아 비인강에서 발생한 점액표피양암종 1례

  • Yoon, Soyeon (Department of Otorhinolaryngology - Head & Neck Surgery, International St. Mary's Hospital, Catholic Kwandong University) ;
  • Kim, Mijoo (Department of Otorhinolaryngology - Head & Neck Surgery, International St. Mary's Hospital, Catholic Kwandong University) ;
  • Kim, Minbum (Department of Otorhinolaryngology - Head & Neck Surgery, International St. Mary's Hospital, Catholic Kwandong University) ;
  • Hong, Hyunjun (Department of Otorhinolaryngology - Head & Neck Surgery, International St. Mary's Hospital, Catholic Kwandong University) ;
  • Song, Keejae (Department of Otorhinolaryngology - Head & Neck Surgery, International St. Mary's Hospital, Catholic Kwandong University)
  • 윤소연 (가톨릭관동대학교 국제성모병원 이비인후-두경부외과) ;
  • 김미주 (가톨릭관동대학교 국제성모병원 이비인후-두경부외과) ;
  • 김민범 (가톨릭관동대학교 국제성모병원 이비인후-두경부외과) ;
  • 홍현준 (가톨릭관동대학교 국제성모병원 이비인후-두경부외과) ;
  • 송기재 (가톨릭관동대학교 국제성모병원 이비인후-두경부외과)
  • Received : 2018.11.02
  • Accepted : 2018.11.07
  • Published : 2018.11.30

Abstract

Malignant salivary gland tumors only represent 0.08% of all childhood tumors. Especially, nasopharyngeal mucoepidermoid carcinoma(MEC) in pediatric age is an extremely rare malignancy. We hereby report a case of nasopharyngeal MEC in 5 year-old female patient. The patient underwent the complete removal of the tumor by endonasal endoscopic approach. Adjuvant postoperative radiotherapy was not considered. After 3.5 years of follow-up, there are no sign of recurrence and metastasis. Minor salivary gland tumor must be considered as a differential diagnosis of angiofibroma in nasopharynx in pediatric age. To our knowledge, the case we describe is the third case of nasopharyngeal MEC in pediatric age reported in literature.

Keywords

References

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