대한영상의학회지 (Journal of the Korean Society of Radiology)

  • 제78권6호
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  • Pages.417-421
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  • 2018
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  • 1738-2637(pISSN)
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  • 2288-2928(eISSN)
대한영상의학회 (The Korean Society of Radiology)
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유아에서 발생한 요추부의 비정형 유기형/간상 종양 증례

Atypical Teratoid/Rhabdoid Tumor of Lumbar Spine in an Infant: A Case Report

  • 송호석 (인제대학교 일산백병원 영상의학과) ;
  • 김용훈 (인제대학교 일산백병원 영상의학과) ;
  • 이지영 (인제대학교 일산백병원 영상의학과) ;
  • 장선희 (인제대학교 일산백병원 병리과) ;
  • 손문준 (인제대학교 일산백병원 신경외과)
  • Song, Hosuk (Department of Radiology, Inje University, Ilsan Paik Hospital) ;
  • Kim, Yonghoon (Department of Radiology, Inje University, Ilsan Paik Hospital) ;
  • Lee, Jiyoung (Department of Radiology, Inje University, Ilsan Paik Hospital) ;
  • Chang, Sunhee (Department of Pathology, Inje University, Ilsan Paik Hospital) ;
  • Sohn, Moonjun (Department of Neurological Surgery, Inje University, Ilsan Paik Hospital)
  • 투고 : 2017.09.09
  • 심사 : 2017.11.23
  • 발행 : 2018.06.01
⟨ 이전 논문 다음 논문 ⟩

초록

척추의 비정형 유기형/간상 종양은 보통 뇌에서 보고되는 드문 종양이다. 간상 세포로 구성되어 있으며 높은 악성도를 가지고 있다. 비정형 유기형/간상 종양은 중추 신경계, 간, 신장, 복부 및 연조직과 같은 전신에 나타난다. 그 중에서도 척추의 비정형 유기형/간상 종양은 드물며, 특히 요추부에 발생하는 비정형 유기형/간상 종양은 매우 드물어 현재까지 몇 케이스만이 보고되었다. 우리는 16개월 소년에서 발생한 요추의 비정형 유기형/간상 종양 증례를 보고한다.

Atypical teratoid/rhabdoid tumor (AT/RT) of spine usually reported to develop in the brain, while it rarely manifest in the spine. It consists of rhabdoid cells and is highly malignant. AT/RT appears at various sites throughout the body, such as in the central nervous system, liver, kidneys, abdomen, and soft tissues. Among them, spinal AT/RT is rare, and AT/RT of lumbar spine is extremely rare; only a few cases have been reported. We present the case of an AT/RT of lumbar spine in a 16-month-old boy.

키워드

참고문헌

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피인용 문헌

  1. Pediatric primary spinal atypical teratoid rhabdoid tumor: a case series and review of the literature vol.24, pp.3, 2018, https://doi.org/10.3171/2019.4.peds19113
  2. Pediatric primary spinal atypical teratoid rhabdoid tumor: a case series and review of the literature vol.24, pp.3, 2018, https://doi.org/10.3171/2019.4.peds19113
  3. Atypical Teratoid/Rhabdoid Tumor of the Conus Medullaris vol.55, pp.4, 2018, https://doi.org/10.1159/000509165