Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Management of Coronary Sinus Ostial Atresia during a Staged Operation of a Functional Single Ventricle

  • Kang, Seung Ri (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Park, Won Kyoun (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kwon, Bo Sang (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Ko, Jae Kon (Division of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Goo, Hyun Woo (Division of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Park, Jeong-Jun (Department of Thoracic and Cardiovascular Surgery, Ewha Womans University Mokdong Hospital, Ewha Womans University School of Medicine)
  • Received : 2017.08.24
  • Accepted : 2017.10.23
  • Published : 2018.04.05
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Abstract

Coronary sinus ostial atresia (CSOA) with persistent left superior vena cava (LSVC) in the absence of an unroofed coronary sinus is a benign and rare anomaly that may be taken lightly in most instances. However, if overlooked in patients undergoing univentricular heart repair such as bidirectional Glenn or Fontan-type surgery, fatal surgical outcomes may occur due to coronary venous drainage failure. We report a case of CSOA with a persistent LSVC that was managed through coronary sinus rerouting during a total cavopulmonary connection, and provide a review of the literature regarding this rare anomaly.

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References

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