Imaging Science in Dentistry

  • 제48권4호
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  • Pages.283-287
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  • 2018
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  • 2233-7822(pISSN)
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  • 2233-7830(eISSN)
대한영상치의학회 (Korean Academy of Oral and Maxillofacial Radiology)
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Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features

  • Yeom, Han-Gyeol (Department of Oral and Maxillofacial Radiology and Dental Research Institute, School of Dentistry, Seoul National University)
  • 투고 : 2018.06.08
  • 심사 : 2018.09.02
  • 발행 : 2018.12.31
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초록

Craniometaphyseal dysplasia (CMD) is a rare hereditary disorder characterized by hyperostosis of the craniofacial bones and flared metaphyses of the long bones. Although some reports have described the dentomaxillofacial characteristics of CMD, including increased density of the jaw, malocclusion, and delayed eruption of the permanent teeth, only a few studies have reported the distinct imaging features of CMD on panoramic radiography. This report presents 2 cases of confirmed CMD patients with an emphasis on panoramic imaging features. The patients' images revealed hyperostosis and sclerosis of the maxilla and mandibular alveolar bone, but there was no change in the mandibular basal bone. In both cases, the mandibular condyle heads exhibited a short clubbed shape with hyperplasia of the coronoid process. For patients without clear otorhinolaryngological symptoms, common radiologic features of CMD could be visualized by routinely-taken panoramic radiographs, and further medical examinations and treatment can be recommended.

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참고문헌

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피인용 문헌

  1. Simultaneous LeFort III and LeFort I Osteotomies in Craniometaphyseal Dysplasia vol.58, pp.12, 2021, https://doi.org/10.1177/1055665621990942