Journal of the korean academy of Pediatric Dentistry (대한소아치과학회지)

Korean Academy of Pediatric Dentistry (대한소아치과학회)
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Dental Treatment in a Patient with CINCA Syndrome under General Anesthesia

CINCA 증후군을 가진 환자의 전신마취 하 치과 치료 : 증례 보고

  • Lee, Ji Min (Department of Pediatric Dentistry, School of Dentistry, Seoul National University) ;
  • Song, Ji-Soo (Department of Pediatric Dentistry, School of Dentistry, Seoul National University) ;
  • Hyun, Hong-Keun (Department of Pediatric Dentistry, School of Dentistry, Seoul National University) ;
  • Kim, Young-Jae (Department of Pediatric Dentistry, School of Dentistry, Seoul National University) ;
  • Kim, Jung-Wook (Department of Pediatric Dentistry, School of Dentistry, Seoul National University) ;
  • Jang, Ki-Taeg (Department of Pediatric Dentistry, School of Dentistry, Seoul National University) ;
  • Lee, Sang-Hoon (Department of Pediatric Dentistry, School of Dentistry, Seoul National University) ;
  • Shin, Teo Jeon (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
  • 이지민 (서울대학교 치의학대학원 소아치과학교실) ;
  • 송지수 (서울대학교 치의학대학원 소아치과학교실) ;
  • 현홍근 (서울대학교 치의학대학원 소아치과학교실) ;
  • 김영재 (서울대학교 치의학대학원 소아치과학교실) ;
  • 김정욱 (서울대학교 치의학대학원 소아치과학교실) ;
  • 장기택 (서울대학교 치의학대학원 소아치과학교실) ;
  • 이상훈 (서울대학교 치의학대학원 소아치과학교실) ;
  • 신터전 (서울대학교 치의학대학원 소아치과학교실)
  • Received : 2017.05.30
  • Accepted : 2017.08.09
  • Published : 2018.02.28
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Abstract

Chronic infantile neurological cutaneous articular (CINCA) syndrome periodically causes fever along with inflammation in multiple organs. Patients with this condition are vulnerable to dental problems due to systemic inflammation. For uncooperative patients, general anesthesia has been widely used to control negative behavior. However, caution should be exercised when administering general anesthesia in these patients because this syndrome is pro-inflammatory. The present case report describes the clinical considerations of the dental treatment of an uncooperative child with CINCA syndrome who was treated under general anesthesia.

Chronic infantile neurological cutaneous articular (CINCA) 증후군은 만성 염증성 질환으로, 주기적으로 발열을 일으킨다. 이 증후군의 환아들은 전신적인 염증으로 인해 치과적 문제에 노출되기 쉽다. 협조가 어려운 환자에 있어서 전신마취는 행동 조절 방법으로 널리 사용되어 왔으며, CINCA 증후군의 경우 전신적인 염증성 질환이기 때문에 전신마취를 시행할 때 있어 주의를 기울어야 한다. 본 증례 보고에서는 CINCA 증후군을 가진 비협조적 환아를 전신마취 하 치과 치료 시행한 증례보고와 함께 이러한 환아들에서 치과치료 전 고려사항을 고찰하고자 한다.

Keywords

References

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