The Journal of Korea Assosiation for Disability and Oral Health (대한장애인치과학회지)

Korean Association for Disability and Oral Health (대한장애인치과학회)
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ALTERNATIVE ORAL REHABILITATION OF A CHILD WITH ECTODERMAL DYSPLASIA: A CASE REPORT

외배엽 이형성증 어린이의 구강 회복: 증례보고

  • Lee, Eungyung (Department of Pediatric Dentistry, School of Dentistry, Pusan National University) ;
  • Kim, Jiyeon (Department of Pediatric Dentistry, School of Dentistry, Pusan National University) ;
  • Kim, Shin (Department of Pediatric Dentistry, School of Dentistry, Pusan National University) ;
  • Jeong, Taesung (Department of Pediatric Dentistry, School of Dentistry, Pusan National University)
  • 이은경 (부산대학교 치의학전문대학원 소아치과학교실) ;
  • 김지연 (부산대학교 치의학전문대학원 소아치과학교실) ;
  • 김신 (부산대학교 치의학전문대학원 소아치과학교실) ;
  • 정태성 (부산대학교 치의학전문대학원 소아치과학교실)
  • Received : 2017.05.22
  • Accepted : 2017.06.19
  • Published : 2017.06.30
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Abstract

Ectodermal Dysplasia is a genetic disorder caused by the abnormal development of two or more structures derived from the ectodermal layer. As an aspect in dentistry, ectodermal dysplasia is characterized by hypodontia, conical or peg-shaped teeth, reduced salivary secretion and decreased vertical dimension. These unfavorable oral conditions make children to have difficulties with mastication, esthetics, and even in social activities. This case report presents an alternative oral rehabilitation treatment of a 4-year-old boy with ectodermal dysplasia. A removable space maintainer with artificial teeth in maxillary arch was delivered according to the initial treatment plan. However, the child failed to adapt the appliance because of his masticatory habit. Then a fixed-type space maintainer was delivered on the patient's esthetic demand and it restored function, esthetics and self-esteem of the patient. The treatment described here suggests that individually customized considerations are essential for the oral rehabilitation of a patient with ectodermal dysplasia.

본 증례에서와 같이 외배엽 이형성증 환자에서는 획일화된 치료 방법은 없다. 술자 입장에서는 기능적 또는 형태적으로 완벽한 장치가 아니라 할지라도, 외배엽 이형성증의 무치악 환아에게는 심미적 요구가 만족됨으로써 자존감을 드높일 수 있는 치료가 될 수 있다. 특히 외배엽 이형성증 환아는 어린 나이에 의치 장착을 시작하기 때문에 환자의 나이와 구강상태, 심미적인 요구 수준, 저작 방법 등 여러가지를 고려한 개별적 맞춤화 과정을 통해 치료방법을 찾는 것이 중요하다. 또한 환자의 성장에 맞춰 장치를 교환해주며 타 과와의 활발한 교류로 최선의 치료를 해주는 것이 추천되며, 술자와 환자 및 환자 보호자간의 충분한 대화를 통해 치료 방법을 신중하게 결정하는 것이 좋다.

Keywords

References

  1. Pinheiro M, Freire-Maia N : Ectodermal dysplasias: a clinical classification and a causal review. Am J Med Genet, 53:153-162, 1994. https://doi.org/10.1002/ajmg.1320530207
  2. Priolo M, Silengo M, Lerone M, et al. : Ectodermal dysplasias: not only' skin'deep. Clin Genet, 58:415-430, 2000.
  3. Halai T, Stevens C : Ectodermal Dysplasia: A Clinical Overview for the Dental Practitioner. Dent Update, 42:779-780, 783-774, 787-778 passim, 2015. https://doi.org/10.12968/denu.2015.42.8.779
  4. Bonilla ED, Guerra L, Luna O : Overdenture prosthesis for oral rehabilitation of hypohidrotic ectodermal dysplasia: a case report. Quintessence Int, 28:657-665, 1997.
  5. Han MG, Kim DH, Moon HR : Herditary Anhidrotic Ectodermal Dysplasia in Twins. J Korean Pediatr Soc, 39:1005-1009, 1996.
  6. Vierucci S, Baccetti T, Tollaro I : Dental and craniofacial findings in hypohidrotic ectodermal dysplasia during the primary dentition phase. The Journal of clinical pediatric dentistry, 18:291-297, 1993.
  7. Lee JG, Yang JH : Longitudinal prosthodontic study of hereditary ectodermal dysplasia: 6 year study. J Korean Acad Prosthodont, 29:249-254, 1991.
  8. Pigno MA, Blackman RB, Cronin RJ, et al. : Prosthodontic management of ectodermal dysplasia: a review of the literature. The Journal of prosthetic dentistry, 76:541-545, 1996. https://doi.org/10.1016/S0022-3913(96)90015-3
  9. Maroulakos G, Artopoulou, II, Angelopoulou MV, et al. : Removable partial dentures vs overdentures in children with ectodermal dysplasia: two case reports. Eur Arch Paediatr Dent, 17:205-210, 2016. https://doi.org/10.1007/s40368-015-0212-x
  10. Pigno MA, Blackman RB, Cronin RJ, Jr., et al. : Prosthodontic management of ectodermal dysplasia: a review of the literature. J Prosthet Dent, 76:541-545, 1996. https://doi.org/10.1016/S0022-3913(96)90015-3
  11. Yap AK, Klineberg I : Dental implants in patients with ectodermal dysplasia and tooth agenesis: a critical review of the literature. Int J Prosthodont, 22:268-276, 2009.
  12. Artopoulou, II, Martin JW, Suchko GD : Prosthodontic rehabilitation of a 10-year-old ectodermal dysplasia patient using provisional implants. Pediatr Dent, 31:52-57, 2009.
  13. Hickey AJ, Salter M : Prosthodontic and psychological factors in treating patients with congenital and craniofacial defects. J Prosthet Dent, 95:392-396, 2006. https://doi.org/10.1016/j.prosdent.2006.03.002
  14. Pope AW, Ward J : Factors associated with peer social competence in preadolescents with craniofacial anomalies. J Pediatr Psychol, 22:455-469, 1997. https://doi.org/10.1093/jpepsy/22.4.455
  15. Endriga MC, Kapp-Simon KA : Psychological issues in craniofacial care: state of the art. Cleft Palate Craniofac J, 36:3-11, 1999. https://doi.org/10.1597/1545-1569(1999)036<0001:PIICCS>2.3.CO;2
  16. Hickey AJ, Vergo TJ, Jr. : Prosthetic treatments for patients with ectodermal dysplasia. J Prosthet Dent, 86:364-368, 2001. https://doi.org/10.1067/mpr.2001.118876