DOI QR코드

DOI QR Code

Fontan Revision with Y-Graft in a Patient with Unilateral Pulmonary Arteriovenous Malformation

  • Lee, Jeong-woo (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Park, Jeong-Jun (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Goo, Hyun Woo (Department of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Ko, Jae Kon (Department of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine)
  • 투고 : 2016.08.29
  • 심사 : 2016.10.28
  • 발행 : 2017.06.05

초록

The extracardiac conduit Fontan procedure is the last surgical step in the treatment of patients with a functional single ventricle. An acquired pulmonary arteriovenous malformation may appear perioperatively or postoperatively due to an uneven hepatic flow distribution. Here we report a case of a bifurcated Y-graft Fontan operation in a 15-year-old male patient with a unilateral pulmonary arteriovenous malformation after an extracardiac conduit Fontan operation.

키워드

참고문헌

  1. Hoffman JI. Normal and abnormal pulmonary arteriovenous shunting: occurrence and mechanisms. Cardiol Young 2013;23:629-41. https://doi.org/10.1017/S1047951113000140
  2. Field-Ridley A, Heljasvaara R, Pihlajaniemi T, et al. Endostatin, an inhibitor of angiogenesis, decreases after bidirectional superior cavopulmonary anastamosis. Pediatr Cardiol 2013;34:291-5. https://doi.org/10.1007/s00246-012-0441-2
  3. Kim SJ, Bae EJ, Lee JY, Lim HG, Lee C, Lee CH. Inclusion of hepatic venous drainage in patients with pulmonary arteriovenous fistulas. Ann Thorac Surg 2009;87:548-53. https://doi.org/10.1016/j.athoracsur.2008.10.024
  4. Imoto Y, Sese A, Joh K. Redirection of the hepatic venous flow for the treatment of pulmonary arteriovenous malformations after Fontan operation. Pediatr Cardiol 2006; 27:490-2. https://doi.org/10.1007/s00246-006-1242-2
  5. McElhinney DB, Marx GR, Marshall AC, Mayer JE, Del Nido PJ. Cavopulmonary pathway modification in patients with heterotaxy and newly diagnosed or persistent pulmonary arteriovenous malformations after a modified Fontan operation. J Thorac Cardiovasc Surg 2011;141:1362-70.e1. https://doi.org/10.1016/j.jtcvs.2010.08.088
  6. Kanter KR, Haggerty CM, Restrepo M, et al. Preliminary clinical experience with a bifurcated Y-graft Fontan procedure: a feasibility study. J Thorac Cardiovasc Surg 2012; 144:383-9. https://doi.org/10.1016/j.jtcvs.2012.05.015
  7. Haggerty CM, Kanter KR, Restrepo M, et al. Simulating hemodynamics of the Fontan Y-graft based on patient-specific in vivo connections. J Thorac Cardiovasc Surg 2013; 145:663-70. https://doi.org/10.1016/j.jtcvs.2012.03.076
  8. Yang W, Chan FP, Reddy VM, Marsden AL, Feinstein JA. Flow simulations and validation for the first cohort of patients undergoing the Y-graft Fontan procedure. J Thorac Cardiovasc Surg 2015;149:247-55. https://doi.org/10.1016/j.jtcvs.2014.08.069

피인용 문헌

  1. Hepatic Vein Incorporation Into the Azygos System in Heterotaxy and Interrupted Inferior Vena Cava vol.10, pp.3, 2019, https://doi.org/10.1177/2150135119842869