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Endoscopic Treatment of Hypothalamic Hamartomas

  • Shim, Kyu Won (Department of Pediatric Neurosurgery, Severance Children's Hospital, Yonsei University College of Medicine, Brain Korea 21 Project for Medical Science) ;
  • Park, Eun Kyung (Department of Pediatric Neurosurgery, Severance Children's Hospital, Yonsei University College of Medicine, Brain Korea 21 Project for Medical Science) ;
  • Kim, Dong-Seok (Department of Pediatric Neurosurgery, Severance Children's Hospital, Yonsei University College of Medicine, Brain Korea 21 Project for Medical Science)
  • 투고 : 2017.01.05
  • 심사 : 2017.03.08
  • 발행 : 2017.05.01

초록

Hypothalamic hamartoma (HH) is a benign indolent lesion despite the presentation of refractory epilepsy. Behavioral disturbances and endocrine problems are additional critical symptoms that arise along with HHs. Due to its nature of generating epileptiform discharge and spreading to cortical region, various management strategies have been proposed and combined. Surgical approaches with open craniotomy or endoscopy, stereotactic approaches with radiosurgery and gamma knife surgery or radiofrequency thermos-coagulation, and laser ablation have been introduced. Topographical dimension and the surgeon's preference are key factors for treatment modalities. Endoscopic disconnection has been one of the most favorable options performed in treating HHs. Here we discuss presurgical evaluation, patient selection, surgical procedures, and complications.

키워드

참고문헌

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피인용 문헌

  1. A Primer on Magnetic Resonance-Guided Laser Interstitial Thermal Therapy for Medically Refractory Epilepsy vol.62, pp.3, 2019, https://doi.org/10.3340/jkns.2019.0105