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Essential Thrombocytosis-Associated Thromboembolism in the Abdominal Aorta

  • Chong, Byung Kwon (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Mun, Dana (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kang, Chae Hoon (Department of Radiology, Gangneung Asan Hospital, University of Ulsan College of Medicine) ;
  • Park, Chong-bin (Department of Thoracic and Cardiovascular Surgery, Gangneung Asan Hospital, University of Ulsan College of Medicine) ;
  • Cho, Won Chul (Department of Thoracic and Cardiovascular Surgery, Gangneung Asan Hospital, University of Ulsan College of Medicine)
  • 투고 : 2015.10.19
  • 심사 : 2016.11.10
  • 발행 : 2016.10.05

초록

Essential thrombocytosis (ET) is a myeloproliferative disorder characterized by an anomalous increase in platelet production. Many patients with ET are asymptomatic. Few studies have reported ET-associated thromboembolism in large vessels such as the aorta. We report a patient with ET who presented with peripheral embolism from an abdominal aortic thrombus and developed acute limb ischemia. The patient underwent aortic replacement successfully. The patient's platelet count was controlled with hydroxyurea, and no recurrence was noted over 2 years of follow-up.

키워드

참고문헌

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  7. Harrison CN, Campbell PJ, Buck G, et al. Hydroxyurea compared with anagrelide in high-risk essential thrombocythemia. N Engl J Med 2005;353:33-45. https://doi.org/10.1056/NEJMoa043800

피인용 문헌

  1. Essential Thrombocythemia Complicated by Occlusive Thrombosis of the Abdominal Aorta vol.2019, pp.None, 2019, https://doi.org/10.1155/2019/9454501
  2. Two effective cases of additional pedal artery angioplasty for severe lower limb ischemia following acute thrombotic artery occlusion with hypercoagulable state diseases vol.3, pp.1, 2016, https://doi.org/10.1186/s42155-020-00166-7