DOI QR코드

DOI QR Code

Three-Dimensional Endo-Cardiovascular Volume-Rendered Cine Computed Tomography of Isolated Left Ventricular Apical Hypoplasia: A Case Report and Literature Review

  • Hong, Sun Hwa (Department of Radiology, Sejong General Hospital) ;
  • Kim, Yang Min (Department of Radiology, Sejong General Hospital) ;
  • Lee, Hyun Jong (Department of Internal Medicine, Division of Cardiology, Sejong General Hospital)
  • 투고 : 2015.06.26
  • 심사 : 2015.09.04
  • 발행 : 2016.02.01

초록

We report multidetector computed tomography (MDCT) and cardiac magnetic resonance (CMR) findings of a 34-year-old female with isolated left ventricular apical hypoplasia. The MDCT and CMR scans displayed a spherical left ventricle (LV) with extensive fatty infiltration within the myocardium at the apex, interventricular septum and inferior wall, anteroapical origin of the papillary muscle, right ventricle wrapping around the deficient LV apex, and impaired systolic function. MDCT visualized morphologic and also functional findings of this unique cardiomyopathy.

키워드

참고문헌

  1. Fernandez-Valls M, Srichai MB, Stillman AE, White RD. Isolated left ventricular apical hypoplasia: a new congenital anomaly described with cardiac tomography. Heart 2004;90:552-555 https://doi.org/10.1136/hrt.2003.010637
  2. Marin C, Sanchez ML, Maroto E, Ossaba S, Ruiz Y, Zabala JI. MR imaging of isolated left ventricular apical hypoplasia. Pediatr Radiol 2007;37:703-705 https://doi.org/10.1007/s00247-007-0459-4
  3. Flett AS, Elliott PM, Moon JC. Images in cardiovascular medicine. Cardiovascular magnetic resonance of isolated left ventricular apical hypoplasia. Circulation 2008;117:e504-e505 https://doi.org/10.1161/CIRCULATIONAHA.107.746503
  4. Irving CA, Chaudhari MP. Fatal presentation of congenital isolated left ventricular apical hypoplasia. Eur J Cardiothorac Surg 2009;35:368-369 https://doi.org/10.1016/j.ejcts.2008.10.039
  5. Patrianakos AP, Protonotarios N, Zacharaki A, Tsatsopoulou A, Parthenakis FI, Vardas PE. Isolated left ventricular apical hypoplasia: a newly recognized unclassified cardiomyopathy. J Am Soc Echocardiogr 2010;23:1336.e1-1336.e4
  6. Haffajee JA, Finley JJ, Brooks EL, Kuvin JT, Patel AR. Echocardiographic characterization of left ventricular apical hypoplasia accompanied by a patent ductus arteriosus. Eur J Echocardiogr 2011;12:E17 https://doi.org/10.1093/ejechocard/jer095
  7. Moon JI, Jeong YJ, Lee G, Choi JH, Lee JW. Isolated left ventricular apical hypoplasia with infundibular pulmonary and aortic stenosis: a rare combination. Korean J Radiol 2013;14:874-877 https://doi.org/10.3348/kjr.2013.14.6.874
  8. Chaowu Y, Xin S, Shihua Z, Jianrong L, Hao W. Complete transposition of the atrioventricular valves associated with left ventricular apical hypoplasia. Circulation 2011;124:e538-e539 https://doi.org/10.1161/CIRCULATIONAHA.111.043620
  9. Motwani M, Witte KK, Plein S, Greenwood JP. Isolated left ventricular apical hypoplasia evaluated by cardiovascular magnetic resonance and gadolinium enhancement techniques. J Am Coll Cardiol 2011;58:2355 https://doi.org/10.1016/j.jacc.2011.02.082
  10. Francone M. Role of cardiac magnetic resonance in the evaluation of dilated cardiomyopathy: diagnostic contribution and prognostic significance. ISRN Radiol 2014;2014:365404
  11. Coats CJ, Quarta G, Flett AS, Pantazis AA, McKenna WJ, Moon JC. Arrhythmogenic left ventricular cardiomyopathy. Circulation 2009;120:2613-2614 https://doi.org/10.1161/CIRCULATIONAHA.109.874628
  12. Paetsch I, Reith S, Gassler N, Jahnke C. Isolated arrhythmogenic left ventricular cardiomyopathy identified by cardiac magnetic resonance imaging. Eur Heart J 2011;32:2840 https://doi.org/10.1093/eurheartj/ehr240

피인용 문헌

  1. User-Friendly Vendor-Specific Guideline for Pediatric Cardiothoracic Computed Tomography Provided by the Asian Society of Cardiovascular Imaging Congenital Heart Disease Study Group: Part 1. Imaging T vol.20, pp.2, 2016, https://doi.org/10.3348/kjr.2018.0571
  2. The results of surgical treatment of a patient with isolated left ventricular apical hypoplasia and left ventricular noncompaction vol.2019, pp.8, 2016, https://doi.org/10.15829/1560-4071-2019-8-97-103
  3. Isolated left ventricular apical hypoplasia with myocardial non-compaction: a case report vol.4, pp.1, 2020, https://doi.org/10.1093/ehjcr/ytz215
  4. Pediatric cardiac computed tomography angiography: Expert consensus from the Filiale de Cardiologie Pédiatrique et Congénitale (FCPC) and the Société Française d vol.101, pp.6, 2016, https://doi.org/10.1016/j.diii.2020.01.007
  5. Cardiac computed tomography angiography in the paediatric population: Expert consensus from the Filiale de cardiologie pédiatrique et congénitale (FCPC) and the Société fra vol.113, pp.8, 2020, https://doi.org/10.1016/j.acvd.2020.03.016