Journal of Yeungnam Medical Science

Yeungnam University College of Medicine, Yeungnam University Institute Medical Science (영남대 의대 학술지 편집위원회)
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Spontaneous renal artery dissection in Ehlers-Danlos syndrome

엘러스-단로스 증후군에 발생한 자발성 신장동맥 박리

  • Lim, Byung-Hun (Department of Internal Medicine, Wonkwang University School of Medicine) ;
  • Lee, Song-I (Department of Internal Medicine, Wonkwang University School of Medicine) ;
  • Lim, Jae-Hong (Department of Internal Medicine, Wonkwang University School of Medicine) ;
  • Oh, Su-Jin (Department of Internal Medicine, Wonkwang University School of Medicine) ;
  • Chu, Min-Su (Department of Internal Medicine, Wonkwang University School of Medicine) ;
  • Ahn, Seon-Ho (Department of Internal Medicine, Wonkwang University School of Medicine) ;
  • Byun, Seung-Jae (Department of Surgery, Wonkwang University School of Medicine)
  • 임병훈 (원광대학교 의과대학 내과학교실) ;
  • 이송이 (원광대학교 의과대학 내과학교실) ;
  • 임재홍 (원광대학교 의과대학 내과학교실) ;
  • 오수진 (원광대학교 의과대학 내과학교실) ;
  • 주민수 (원광대학교 의과대학 내과학교실) ;
  • 안선호 (원광대학교 의과대학 내과학교실) ;
  • 변승재 (원광대학교 의과대학 외과학교실)
  • Received : 2014.12.11
  • Accepted : 2015.03.19
  • Published : 2016.06.30
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Abstract

Primary dissection of the renal artery is rare. Spontaneous renal artery dissection can be associated with diseases such as medial degeneration, neurofibromatosis, syphilitic arteritis, tuberculosis, polyarteritis nodosa, Marfan syndrome, fibromuscular dysplasia, or Ehlers-Danlos syndrome (EDS). Among these causes, EDS related renal artery dissection is very rare worldwide and has not been previously reported in Korea. EDS are a group of heritable connective tissue disorders characterized by fragility of the skin and hypermobility of the joints. We describe the case history of a young man who presented with left side flank pain, hypermobility of the hand joints and showed left renal artery dissection on computed tomography and angiography that turned out to be the first complication of vascular type EDS.

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References

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