DOI QR코드

DOI QR Code

Right Atrial Paraganglioma: An Extremely Rare Primary Cardiac Neoplasm Mimicking Myxoma

  • Garg, Ashok (Department of Non-invasive Cardiology, Jaipur Heart Institute) ;
  • Mishra, Deepika (Department of Pathology, SMS Medical College) ;
  • Bansal, Manish (Department of Cardiology, Medanta-The Medicity) ;
  • Maharia, Hari Ram (Department of Cardiology, Metro MAS Hospital) ;
  • Goyal, Vikram (Departments of Cardiothoracic Surgery, Jaipur Heart Institute)
  • 투고 : 2016.07.18
  • 심사 : 2016.11.30
  • 발행 : 2016.12.27

초록

In this report, we present a case of 35-year-old lady who had presented with atypical chest pain and exertional breathlessness for past six months. Transthoracic and transesophageal echocardiograms showed a well-circumscribed, echo-dense mass in the right atrium, attached to the interatrial septum at the level of atrioventricular junction and in the vicinity of coronary sinus ostium. She underwent successful resection of the cardiac mass. Histopathology revealed paraganglioma, which was reconfirmed by immunohistochemistry study. This represents an extremely rare presentation as primary cardiac tumors are 20-times less common than metastatic tumors and paraganglioma is one of the rarest primary cardiac tumors, accounting for < 1% of all cases.

키워드

참고문헌

  1. Tahir M, Noor SJ, Herle A, Downing S. Right atrial paraganglioma: a rare primary cardiac neoplasm as a cause of chest pain. Tex Heart Inst J 2009;36:594-7.
  2. Maxey TS, Grow P, Morris CD, Patton KT, Guyton RA. Biatrial primary cardiac paraganglioma: a rare finding. Cardiovasc Pathol 2007;16:179-82. https://doi.org/10.1016/j.carpath.2006.11.002
  3. Jeevanandam V, Oz MC, Shapiro B, Barr ML, Marboe C, Rose EA. Surgical management of cardiac pheochromocytoma. Resection versus transplantation. Ann Surg 1995;221:415-9. https://doi.org/10.1097/00000658-199504000-00013
  4. Okum EJ, Henry D, Kasirajan V, Deanda A. Cardiac pheochromocytoma. J Thorac Cardiovasc Surg 2005;129:674-5. https://doi.org/10.1016/j.jtcvs.2004.07.028
  5. Kennelly R, Aziz R, Toner M, Young V. Right atrial paraganglioma: an unusual primary cardiac tumour. Eur J Cardiothorac Surg 2008;33:1150-2. https://doi.org/10.1016/j.ejcts.2008.02.031
  6. Hayek ER, Hughes MM, Speakman ED, Miller HJ, Stocker PJ. Cardiac paraganglioma presenting with acute myocardial infarction and stroke. Ann Thorac Surg 2007;83:1882-4. https://doi.org/10.1016/j.athoracsur.2006.12.023
  7. Brown IE, Milshteyn M, Kleinman B, Bakhos M, Roizen MF, Jeevanandam V. Case 3--2002. Pheochromocytoma presenting as a right intra-atrial mass. J Cardiothorac Vasc Anesth 2002;16:370-3. https://doi.org/10.1053/jcan.2002.124151
  8. Palubinskas AJ, Roizen MF, Conte FA. Localization of functioning pheochromocytomas by venous sampling and radioenzymatic analysis. Radiology 1980;136:495-6. https://doi.org/10.1148/radiology.136.2.7403529
  9. Kawasuji M, Matsunaga Y, Iwa T. Cardiac phaeochromocytoma of the interatrial septum. Eur J Cardiothorac Surg 1989;3:175-7. https://doi.org/10.1016/1010-7940(89)90098-5
  10. Joynt KE, Moslehi JJ, Baughman KL. Paragangliomas: etiology, presentation, and management. Cardiol Rev 2009;17:159-64. https://doi.org/10.1097/CRD.0b013e3181a6de40

피인용 문헌

  1. Update on Adrenal Tumours in 2017 World Health Organization (WHO) of Endocrine Tumours vol.28, pp.3, 2016, https://doi.org/10.1007/s12022-017-9484-5
  2. Imaging of Intrathoracic Paragangliomas vol.38, pp.6, 2016, https://doi.org/10.1053/j.sult.2017.07.004
  3. A patient with paraganglioma undergoing laparoscopic resection: A case report vol.9, pp.6, 2016, https://doi.org/10.1002/ccr3.4145