Journal of Cardiovascular Imaging

Korean Society of Echocardiography (한국심초음파학회)
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Right Atrial Paraganglioma: An Extremely Rare Primary Cardiac Neoplasm Mimicking Myxoma

  • Garg, Ashok (Department of Non-invasive Cardiology, Jaipur Heart Institute) ;
  • Mishra, Deepika (Department of Pathology, SMS Medical College) ;
  • Bansal, Manish (Department of Cardiology, Medanta-The Medicity) ;
  • Maharia, Hari Ram (Department of Cardiology, Metro MAS Hospital) ;
  • Goyal, Vikram (Departments of Cardiothoracic Surgery, Jaipur Heart Institute)
  • Received : 2016.07.18
  • Accepted : 2016.11.30
  • Published : 2016.12.27
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Abstract

In this report, we present a case of 35-year-old lady who had presented with atypical chest pain and exertional breathlessness for past six months. Transthoracic and transesophageal echocardiograms showed a well-circumscribed, echo-dense mass in the right atrium, attached to the interatrial septum at the level of atrioventricular junction and in the vicinity of coronary sinus ostium. She underwent successful resection of the cardiac mass. Histopathology revealed paraganglioma, which was reconfirmed by immunohistochemistry study. This represents an extremely rare presentation as primary cardiac tumors are 20-times less common than metastatic tumors and paraganglioma is one of the rarest primary cardiac tumors, accounting for < 1% of all cases.

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References

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