The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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Isolated Right Ventricular Noncompaction Accompanied by Right Ventricular Failure

우심실부전이 동반된 단독우심실비치밀화증

  • Lim, Sanghyok (Department of Internal Medicine, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine) ;
  • Ahn, Jihun (Department of Internal Medicine, Soonchunhyang University Gumi Hospital, Soonchunhyang University College of Medicine) ;
  • O, Taehun (Department of Internal Medicine, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine) ;
  • Lee, Donghyun (Department of Internal Medicine, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine) ;
  • Park, Minwoo (Department of Internal Medicine, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine)
  • 임상혁 (순천향대학교 의과대학 순천향대학교 천안병원 내과) ;
  • 안지훈 (순천향대학교 의과대학 순천향대학교 구미병원 내과) ;
  • 오태훈 (순천향대학교 의과대학 순천향대학교 천안병원 내과) ;
  • 이동현 (순천향대학교 의과대학 순천향대학교 천안병원 내과) ;
  • 박민우 (순천향대학교 의과대학 순천향대학교 천안병원 내과)
  • Published : 20150000
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Abstract

Noncompaction of the ventricular myocardium is a rare congenital cardiomyopathy caused by arrest of normal endomyocardial embryogenesis. Isolated right ventricular noncompaction (IRNC) is an even rarer form of this disease. We report herein on a 68 year-old male diagnosed with IRNC who presented with right-sided heart failure, without involvement of the left ventricle. Diagnosis was achieved with the aid of echocardiography and ventriculography. Medical treatment including prescription of diuretics, a calcium channel blocker, and digitalis, improved both the symptoms and right ventricular function.

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