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A군 사슬알균 감염 후 사구체신염 환아에서 발생한 가역적 후두부 뇌병증 증후군 1례

A Case of Posterior Reversible Leukoencephalopathy Syndrome Following Poststreptococcal Glomerulonephritis

  • 이은경 (가톨릭대학교 의과대학 소아과학교실) ;
  • 강진한 (가톨릭대학교 의과대학 소아과학교실) ;
  • 마상혁 (창원파티마병원 소아청소년과)
  • Lee, Eun Kyoung (Department of Pediatrics, The Catholic University of Korea College of Medicine) ;
  • Kang, Jin Han (Department of Pediatrics, The Catholic University of Korea College of Medicine) ;
  • Ma, Sang Hyuk (Department of Pediatrics, Fatima Hospital)
  • 투고 : 2015.05.08
  • 심사 : 2015.06.08
  • 발행 : 2015.08.25

초록

가역적 후두부 뇌병증 증후군은 다양한 원인에 의하여 생기는 발생하는 질환으로 갑자기 생기는 두통, 정신상태의 변화, 시력장애, 경련 등이 주증상이다. 영상의학 검사에서는 후두부 백질의 부종이 양측성 혹은 일측성으로 나타난다. 저자들은 A군 사슬알균 감염 후 가역적 후두부 뇌병증 증후군을 보인 환자를 경험하였고 고혈압을 조절한 후 환자는 빠른 시간 내에 신경학적인 회복을 보였다.

Posterior reversible leukoencephalopathy syndrome is a clinical radiographic syndrome of many causative factors. Sudden onset headache, vomiting, altered mental status, blurred vision and seizures are main symptoms shown in posterior reversible leukoencephalopathy syndrome. In addition, it typically shows radiological findings of edema in the white matter of posterior cerebrum, being in commonly bilateral but asymmetric. We report a case of poststreptococcal glomerulonephritis (PSGN) presenting as posterior reversible leukoencephalopathy syndrome. Immediate control of hypertension resulted in rapid and complete neurological recovery.

키워드

참고문헌

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