The Journal of Advanced Prosthodontics

The Korean Academy of Prosthodonitics (대한치과보철학회)
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Familial gigantiform cementoma with Ehlers - Danlos syndrome: A report of 2 cases

  • Sakar, Olcay (Department of Prosthodontics, School of Dentistry, Istanbul University) ;
  • Aren, Gamze (Department of Pedodontics, Faculty of Dentistry, Istanbul University) ;
  • Mumcu, Zeynep (Department of Prosthodontics, School of Dentistry, Istanbul University) ;
  • Unalan, Fatma (Department of Prosthodontics, School of Dentistry, Istanbul University) ;
  • Aksakalli, Nihan (Institute of Oncology, Faculty of Medicine, Istanbul University) ;
  • Tolgay, Ceren Guney (Department of Pedodontics, Faculty of Dentistry, Istanbul University)
  • Received : 2014.08.27
  • Accepted : 2015.03.05
  • Published : 2015.04.30
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Abstract

Ehlers-Danlos syndrome is an autosomal dominant hereditary disorder of connective tissue, while familial gigantiform cementoma is a condition that usually manifests as multiple radiopaque cementum-like masses throughout the jaws. This case report discusses the oral management and prosthetic rehabilitation of two patients presenting familial gigantiform cementoma with Ehlers-Danlos Syndrome.

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References

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