Investigative Magnetic Resonance Imaging

  • 제19권3호
  • /
  • Pages.196-199
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  • 2015
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  • 2384-1095(pISSN)
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  • 2384-1109(eISSN)
대한자기공명의과학회 (Korean Society of Magnetic Resonance in Medicine)
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MRI Findings of Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA syndrome) with a Blind Megaureter: Case Report

  • Cho, Yun Hee (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Sung, Deuk Jae (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Han, Na Yeon (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Park, Beom Jin (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Kim, Min Ju (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Sim, Ki Choon (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Cho, Sung Bum (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University)
  • 투고 : 2015.07.19
  • 심사 : 2015.08.27
  • 발행 : 2015.09.30
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초록

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is an uncommon congenital abnormality of the female urogenital tract characterized by the triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. A 13-year-old female presented with acute lower abdominal pain. Magnetic resonance imaging (MRI) revealed uterine didelphys, hematometrocolpos, obstructed hemivagina, and right ipsilateral agenesis, consistent with OHVIRA syndrome. Also, a well-defined mass with fluid signal intensity, mimicking adnexal neoplasm was seen in the right lower pelvic cavity adjacent to the posterior wall of the bladder. Vaginal septotomy and drainage of hematometrocolpos were done initially, but unilateral hysterectomy was later performed to relieve the patient's symptoms. The cystic mass in the right lower pelvic cavity was also excised and confirmed as a blind megaureter.

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참고문헌

  1. Lopes Dias J, Jogo R. Herlyn-Werner-Wunderlich syndrome: pre- and post-surgical MRI and US findings. Abdom Imaging 2015 [Epub ahead of print]
  2. Orazi C, Lucchetti MC, Schingo PM, Marchetti P, Ferro F. Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases. Pediatr Radiol 2007;37:657-665 https://doi.org/10.1007/s00247-007-0497-y
  3. Del Vescovo R, Battisti S, Di Paola V, et al. Herlyn-Werner-Wunderlich syndrome: MRI findings, radiological guide (two cases and literature review), and differential diagnosis. BMC Med Imaging 2012;12:4 https://doi.org/10.1186/1471-2342-12-4
  4. Behr SC, Courtier JL, Qayyum A. Imaging of mullerian duct anomalies. Radiographics 2012;32:E233-250 https://doi.org/10.1148/rg.326125515
  5. Smith NA, Laufer MR. Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: management and follow-up. Fertil Steril 2007;87:918-922 https://doi.org/10.1016/j.fertnstert.2006.11.015
  6. Dobrocky I, Motoska V, Kemka S, Mistina l'U. Ectopic blind ureter with ipsilateral renal agenesis: a case report. Eur J Radiol 1995;20:77-79 https://doi.org/10.1016/0720-048X(95)00629-5
  7. La Fianza A, Preda L, Di Maggio EM, Campani R. Blind megaureter with ipsilateral renal agenesis and mullerian anomaly: MR findings in a case. Clin Imaging 1999;23:184-186 https://doi.org/10.1016/S0899-7071(99)00114-X
  8. Han B, Herndon CN, Rosen MP, Wang ZJ, Daldrup-Link H. Uterine didelphys associated with obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome. Radiology Case Reports 2010;5:327 https://doi.org/10.2484/rcr.v5i1.327
  9. Donnez O, Jadoul P, Squifflet J, Donnez J. Didelphic uterus and obstructed hemivagina: recurrent hematometra in spite of appropriate classic surgical treatment. Gynecol Obstet Invest 2007;63:98-101 https://doi.org/10.1159/000096015

피인용 문헌

  1. Two Cases of Herlyn-Werner-Wunderlich Syndrome in Neonates and Adolescents with Hydrocolpos and Hematocolpometra vol.30, pp.4, 2015, https://doi.org/10.14734/pn.2019.30.4.236